Introduction Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive, and irreversible
fibrotic disease associated with respiratory failure. The disease remains idiopathic, but …

Background We have previously reported arterial remodelling in patients with idiopathic
pulmonary fibrosis (IPF) and suggested that endothelial-to-mesenchymal transition (EndMT) …

Pulmonary hypertension (PH) developing secondarily in pulmonary fibrosis (PF) patients
(PF-PH) is a frequent co-morbidity. The high prevalence of PH in PF patients is very …

Idiopathic pulmonary fibrosis (IPF) is a disabling disease of the lung parenchyma,
characterized by progressive accumulation of scar tissue and myofibroblast activation after …

Idiopathic pulmonary fibrosis (IPF) is a progressive and irreversible fibrosing interstitial
pneumonia of unknown aetiology that usually leads to respiratory failure and death within 5 …

Idiopathic pulmonary fibrosis (IPF) is a serious disease of the lung, which leads to extensive
parenchymal scarring and death from respiratory failure. The most accepted hypothesis for …

Idiopathic pulmonary fibrosis (IPF) is a progressive scarring disease of the lung with poor
survival. The incidence and mortality of IPF are rising, but treatment remains limited …

Pulmonary fibrosis (PF) encompasses a spectrum of chronic lung diseases that
progressively impact the interstitium, resulting in compromised gas exchange …

Abstract Background and Aim Idiopathic pulmonary fibrosis (IPF) is characterized by
hyperplasia of type II alveolar epithelial cells, aggregation of activated (myo) fibroblasts and …

Highlights What are the main findings? We reviewed the latest advances in aberrant
molecular events and pathological alterations in different cell populations in idiopathic …