Assessment of extracellular volume fraction in Becker muscular dystrophy by using MR fingerprinting

B Marty, PY Baudin, E Caldas de Almeida Araujo… - Radiology, 2023 - pubs.rsna.org
Background Quantitative MRI is increasingly proposed in clinical trials related to
dystrophinopathies, including Becker muscular dystrophy (BMD). Purpose To establish the …

Quantitative muscle MRI protocol as possible biomarker in Becker muscular dystrophy

L Maggi, M Moscatelli, R Frangiamore, F Mazzi… - Clinical …, 2021 - Springer
Purpose Aim of this study is to compare Quantitative Magnetic Resonance Imaging (qMRI)
measures between Becker Muscular Dystrophy (BMD) and Healthy Subjects (HS) and to …

[HTML][HTML] Quantitative muscle MRI as outcome measure in patients with Becker muscular dystrophy—A 1-year follow-up study

AM Sheikh, K Rudolf, N Witting, J Vissing - Frontiers in Neurology, 2021 - frontiersin.org
Introduction: With the advent of emerging molecular therapies for muscular dystrophies, the
need for knowledge about natural history course of such diseases is of utmost importance in …

Diffusion‐tensor magnetic resonance imaging captures increased skeletal muscle fibre diameters in Becker muscular dystrophy

D Cameron, T Abbassi‐Daloii… - Journal of cachexia …, 2023 - Wiley Online Library
Background Becker muscular dystrophy (BMD) is an X‐linked disorder characterized by
slow, progressive muscle damage and muscle weakness. Hallmarks include fibre‐size …

Calf muscle involvement in Becker muscular dystrophy: when size does not matter

M Monforte, E Mercuri, F Laschena, E Ricci… - Journal of the …, 2014 - Elsevier
Introduction Calf hypertrophy is a common feature in Becker muscular dystrophy (BMD), and
it is still debated to which extent fatty degeneration or true muscle hypertrophy account for it …

Selection approach to identify the optimal biomarker using quantitative muscle MRI and functional assessments in Becker muscular dystrophy

NM van de Velde, MT Hooijmans… - Neurology, 2021 - AAN Enterprises
Objective To identify the best quantitative fat–water MRI biomarker for disease progression
of leg muscles in Becker muscular dystrophy (BMD) by applying a stepwise approach based …

Baseline fat fraction is a strong predictor of disease progression in Becker muscular dystrophy

TTJ Veeger, NM van de Velde, KR Keene… - NMR in …, 2022 - Wiley Online Library
In Becker muscular dystrophy (BMD), muscle weakness progresses relatively slowly, with a
highly variable rate among patients. This complicates clinical trials, as clinically relevant …

Characterization of patients with Becker muscular dystrophy by histology, magnetic resonance imaging, function, and strength assessments

GP Comi, EH Niks, CM Cinnante, HE Kan… - Muscle & …, 2022 - Wiley Online Library
Abstract Introduction/Aims Becker muscular dystrophy (BMD) is characterized by variable
disease severity and progression, prompting the identification of biomarkers for clinical trials …

Muscle MRS detects elevated PDE/ATP ratios prior to fatty infiltration in Becker muscular dystrophy

BH Wokke, MT Hooijmans… - NMR in …, 2014 - Wiley Online Library
Becker muscular dystrophy (BMD) is characterized by progressive muscle weakness.
Muscles show structural changes (fatty infiltration, fibrosis) and metabolic changes, both of …

[HTML][HTML] Muscle MRI and functional outcome measures in Becker muscular dystrophy

A Barp, L Bello, L Caumo, P Campadello… - Scientific Reports, 2017 - nature.com
Becker muscular dystrophy (BMD) is a neuromuscular disorder allelic to Duchenne
muscular dystrophy (DMD), caused by in-frame mutations in the dystrophin gene, and …