A number of genetic syndromes have been linked to increased risk for Wilms tumor (WT),
hepatoblastoma (HB), and other embryonal tumors. Here, we outline these rare syndromes …

Background We undertook a cost‐benefit analysis of screening for Wilms tumor and
hepatoblastoma in children with Beckwith‐Wiedemann syndrome (BWS), a known cancer …

Background: Most Wilms tumours occur in otherwise healthy children, but a small proportion
occur in children with genetic syndromes associated with increased risks of Wilms tumour …

Hereditary gastrointestinal cancer predisposition syndromes have been well characterized,
but management strategies and surveillance remain a major challenge, especially in …

Background Hepatoblastoma (HB) is the most frequent liver tumor in childhood, occurring in
the first few years of life. Surgery combined with chemotherapy has resulted in dramatic …

Abstract Background Wilms Tumor (WT) can occur in association with tumor predisposition
syndromes and/or with clinical malformations. These associations have not been fully …

Abstract Background Children with Beckwith‐Wiedemann syndrome and idiopathic
hemihypertrophy (BWS/HH) are at increased risk for developing Wilms tumor and screening …

Few causes of hepatoblastoma have been conclusively identified, mainly due to the extreme
rarity of the disease. Inherited conditions including Familial Adenomatous Polyposis and …

Wilms tumor can occur in association with a number of recognizable patterns of
malformation, as first described by Miller et al. in 1964 [1]. This paper represents a synthesis …

Improvements in our understanding of the genetic basis of human disease and increased
utilization of genetic testing have identified a variety of heritable disorders associated with …