Prognostic value of follow-up hemodynamic variables after initial management in pulmonary arterial hypertension

J Weatherald, A Boucly, D Chemla, L Savale, M Peng… - Circulation, 2018 - Am Heart Assoc
Background: Hemodynamic variables such as cardiac index and right atrial pressure have
consistently been associated with survival in pulmonary arterial hypertension (PAH) at the …

Predicting survival in pulmonary arterial hypertension: insights from the registry to evaluate early and long-term pulmonary arterial hypertension disease management …

RL Benza, DP Miller, M Gomberg-Maitland, RP Frantz… - Circulation, 2010 - Am Heart Assoc
Background—Factors that determine survival in pulmonary arterial hypertension (PAH) drive
clinical management. A quantitative survival prediction tool has not been established for …

Evaluation of the predictive value of a clinical worsening definition using 2-year outcomes in patients with pulmonary arterial hypertension: a REVEAL Registry …

AE Frost, DB Badesch, DP Miller, RL Benza, LA Meltzer… - Chest, 2013 - Elsevier
Background Time to clinical worsening has been proposed as a primary end point in clinical
trials of pulmonary arterial hypertension (PAH); however, neither standardized nor validated …

Risk assessment, prognosis and guideline implementation in pulmonary arterial hypertension

A Boucly, J Weatherald, L Savale, X Jaïs… - European …, 2017 - Eur Respiratory Soc
Current European guidelines recommend periodic risk assessment for patients with
pulmonary arterial hypertension (PAH). The aim of our study was to determine the …

The prognostic impact of follow-up assessments in patients with idiopathic pulmonary arterial hypertension

N Nickel, H Golpon, M Greer, L Knudsen… - European …, 2012 - Eur Respiratory Soc
Current guidelines for the treatment of patients with idiopathic pulmonary arterial
hypertension (IPAH) recommend basing therapeutic decision-making on haemodynamic …

Integration of clinical and hemodynamic parameters in the prediction of long-term survival in patients with pulmonary arterial hypertension

GC Kane, H Maradit-Kremers, JP Slusser, CG Scott… - Chest, 2011 - Elsevier
Background Current management guidelines for pulmonary arterial hypertension (PAH)
recommend a treatment choice based primarily on World Health Organization (WHO) …

Association between initial treatment strategy and long-term survival in pulmonary arterial hypertension

A Boucly, L Savale, X Jaïs, F Bauer… - American journal of …, 2021 - atsjournals.org
Rationale: The relationship between the initial treatment strategy and survival in pulmonary
arterial hypertension (PAH) remains uncertain. Objectives: To evaluate the long-term …

Prognosis of pulmonary arterial hypertension*: ACCP evidence-based clinical practice guidelines

VV McLaughlin, KW Presberg, RL Doyle, SH Abman… - Chest, 2004 - Elsevier
Although idiopathic pulmonary arterial hypertension is perceived as a progressive disease
with a uniformly poor outcome, the natural history of disease is heterogeneous, with some …

[HTML][HTML] Prognostic implications of serial risk score assessments in patients with pulmonary arterial hypertension: a Registry to Evaluate Early and Long-Term …

RL Benza, DP Miller, AJ Foreman, AE Frost… - The Journal of Heart and …, 2015 - Elsevier
Background Data from the Registry to Evaluate Early and Long-Term Pulmonary Arterial
Hypertension Disease Management (REVEAL) were used previously to develop a risk score …

An evaluation of long-term survival from time of diagnosis in pulmonary arterial hypertension from the REVEAL Registry

RL Benza, DP Miller, RJ Barst, DB Badesch, AE Frost… - Chest, 2012 - Elsevier
Background The Registry to Evaluate Early and Long-term Pulmonary Arterial Hypertension
Disease Management (REVEAL Registry) was established to characterize the clinical …