Objective Cardiac disease accounts for a large burden of premature mortality and morbidity
in patients with type 1 myotonic dystrophy (MD). However, little is known about structural …

Background Myotonic dystrophy type 1 (MD1) is a neuromuscular disorder with potential
involvement of the heart and increased risk of sudden death. Considering the importance of …

Background Patients with myotonic dystrophy type 1 (DM1) have a three-fold higher risk of
sudden cardiac death (SCD) than age-matched healthy controls. Despite numerous …

BACKGROUND: Myotonic dystrophy type 1 (DM1) is a neurological disorder with known
cardiac involvement, including conduction disturbances, arrhythmias, and ventricular …

Aims To quantify the association between myotonic dystrophy (DM) and cardiac disease in a
nationwide cohort. Methods and results We identified a nationwide cohort of 1146 DM …

AIMS: To estimate the degree of cardiac involvement regarding left ventricular ejection
fraction, conduction abnormalities, arrhythmia, risk of sudden cardiac death (SCD) and the …

Background Frequency and severity of cardiac involvement in DM2 are still controversial.
The aims of our study were to determine the frequency and progression of cardiac and …

OBJECTIVE: The aim of the study was to identify, in addition to conduction defects, possible
predictors of cardiac events and death in patients with myotonic dystrophy (DM1) …

Background Cardiac involvement in myotonic dystrophy type 1 (MD1) includes conduction
disease, arrhythmias, and left-ventricular (LV) systolic dysfunction leading to an increased …

BACKGROUND: Myotonic dystrophy type 1 (DM1) is a systemic disease which affects the
heart and may be a cause of sudden death. Conduction disturbances are the major cardiac …