Pleuroparenchymal fibroelastosis

V Cottin, S Si-Mohamed, R Diesler… - Current Opinion in …, 2022 - journals.lww.com
Pleuroparenchymal fibroelastosis : Current Opinion in Pulmonary Medicine
Pleuroparenchymal fibroelastosis : Current Opinion in Pulmonary Medicine Log in or …

Pleuroparenchymal fibroelastosis: its clinical characteristics

K Watanabe - Current respiratory medicine reviews, 2013 - ingentaconnect.com
Pleuroparenchymal fibroelastosis (PPFE) is a rare pulmonary fibrosis that is clinically
characterized by upperlobe predominant fibrosis. PPFE is a slowly progressive disorder and …

[HTML][HTML] Disease course and prognosis of pleuroparenchymal fibroelastosis compared with idiopathic pulmonary fibrosis

Y Suzuki, T Fujisawa, H Sumikawa, T Tanaka… - Respiratory …, 2020 - Elsevier
Background Idiopathic pleuroparenchymal fibroelastosis (iPPFE) is a rare interstitial lung
disease characterized by unique radiological and pathological findings. However …

[HTML][HTML] Comparison of clinical characteristics and outcomes between idiopathic and secondary pleuroparenchymal fibroelastosis

T Oda, A Sekine, E Tabata, T Iwasawa… - Journal of Clinical …, 2021 - mdpi.com
Background: Pleuroparenchymal fibroelastosis (PPFE) is a unique clinical, radiologic, and
histopathologic entity for which several potential etiologies have been reported recently …

Pleuroparenchymal fibroelastosis: so many unmet needs

P Bonniaud, V Cottin, G Beltramo - European Respiratory …, 2022 - Eur Respiratory Soc
Pleuroparenchymal fibroelastosis (PPFE) is a severe clinical entity that was only identified at
the turn of the 21st century. There are so many unanswered questions and clinical …

Poorer prognosis of idiopathic pleuroparenchymal fibroelastosis compared with idiopathic pulmonary fibrosis in advanced stage

M Shioya, M Otsuka, G Yamada… - Canadian respiratory …, 2018 - Wiley Online Library
Objective. Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare disease
characterized by predominant upper lobe pulmonary fibrosis of unknown etiology. However …

[HTML][HTML] Idiopathic pleuroparenchymal fibroelastosis

M Bonifazi, MA Montero, EA Renzoni - Current Pulmonology Reports, 2017 - Springer
Purpose of the review Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare fibrosing
lung disease, affecting the visceral pleura and the subpleural parenchyma with an upper …

Idiopathic pleuroparenchymal fibroelastosis: three-dimensional computed tomography assessment of upper-lobe lung volume

A Fukada, Y Suzuki, K Mori, M Kono… - European …, 2022 - Eur Respiratory Soc
Background Idiopathic pleuroparenchymal fibroelastosis (iPPFE) is a rare interstitial lung
disease characterised by predominant upper-lobe fibrosis involving the pleura and …

[HTML][HTML] Pleuroparenchymal fibroelastosis: clinical, radiological and histopathological features

J Ricoy, J Suárez-Antelo, J Antúnez, AM de Alegría… - Respiratory …, 2022 - Elsevier
Pleuroparenchymal fibroelastosis (PPFE) is a rare, generally idiopathic form of interstitial
pneumonia with unique clinical, radiological and histopathological features. It is named after …

[HTML][HTML] Clinical diagnosis of idiopathic pleuroparenchymal fibroelastosis: a retrospective multicenter study

Y Enomoto, Y Nakamura, Y Satake, H Sumikawa… - Respiratory …, 2017 - Elsevier
Background Although the accurate diagnosis of pleuroparenchymal fibroelastosis (PPFE)
requires pathologic evaluation, this diagnosis is often suggested when the radiologic …