Left ventricular dysfunction and cardiac arrhythmias are frequent in type 2 myotonic dystrophy: a case control study

K Wahbi, C Meune, HM Bécane, P Laforêt… - Neuromuscular …, 2009 - Elsevier
In contrast with Steinert's disease (DM1), type 2 muscular dystrophy (DM2) is not known to
be associated with a high prevalence of cardiac involvement. Our objective was to compare …

Natural history of cardiac involvement in myotonic dystrophy (Steinert's disease): a 13-year follow-up study

A Mammarella, M Paradiso, G Antonini, V Paoletti… - Advances in …, 2000 - Springer
Myotonic dystrophy (MD) is associated with a wide spectrum of cardiac abnormalities, but
only a few longitudinal studies have investigated the natural course of heart disease in MD …

Cardiac involvement in Steinert's myotonic dystrophy

S Chebel, A Boughammoura, BF MH - Revue neurologique, 2005 - europepmc.org
[Cardiac involvement in Steinert's myotonic dystrophy]. - Abstract - Europe PMC Sign in | Create
an account https://orcid.org Europe PMC Menu About Tools Developers Help Contact us …

Myotonic dystrophy and the heart

G Pelargonio, AD Russo, T Sanna, G De Martino… - Heart, 2002 - heart.bmj.com
Myotonic dystrophy (dystrophia myotonica, DM) is the most frequently inherited
neuromuscular disease of adult life. DM is a multisystem disease with major cardiac …

The frequency and severity of cardiac involvement in myotonic dystrophy type 2 (DM2): long-term outcomes

VA Sansone, E Brigonzi, B Schoser, S Villani… - International journal of …, 2013 - Elsevier
Background Frequency and severity of cardiac involvement in DM2 are still controversial.
The aims of our study were to determine the frequency and progression of cardiac and …

[HTML][HTML] The heart and cardiac pacing in Steinert disease

G Nigro, AA Papa, L Politano - Acta Myologica, 2012 - ncbi.nlm.nih.gov
Abstract Myotonic dystrophy (Dystrophia Myotonica, DM) is the most frequently inherited
neuromuscular disease of adult life. It is a multisystemic disease with major cardiac …

Heart involvement in patients with myotonic dystrophy type 2

S Peric, B Bjelica, K Aleksic, M Kovacevic… - Acta Neurologica …, 2019 - Springer
Abstract Myotonic dystrophy type 2 (DM2) is a slowly progressive, autosomal-dominant
disease. This is a multisystemic disorder that affects the heart, which is one of the main …

Clinical and molecular aspects of the myotonic dystrophies: a review

L Machuca‐Tzili, D Brook… - Muscle & Nerve: Official …, 2005 - Wiley Online Library
Type 1 myotonic dystrophy or DM1 (Steinert's disease), which is the commonest muscular
dystrophy in adults, has intrigued physicians for over a century. Unusual features, compared …

Survival and mortality of myotonic dystrophy type 1 (Steinert's disease) in the population of Belgrade

J Mladenovic, T Pekmezovic… - European Journal of …, 2006 - Wiley Online Library
The purpose of this investigation was to determine survival and mortality in patients with
myotonic dystrophy type 1 (DM1) in the Belgrade population within the period from 1983 to …

Incidence and predictors of sudden death, major conduction defects and sustained ventricular tachyarrhythmias in 1388 patients with myotonic dystrophy type 1

K Wahbi, D Babuty, V Probst, L Wissocque… - European heart …, 2017 - academic.oup.com
Aims To describe the incidence and identify predictors of sudden death (SD), major
conduction defects and sustained ventricular tachyarrhythmias (VTA) in myotonic dystrophy …