Sudden cardiac death in neuromuscular disorders

J Finsterer, C Stöllberger, C Maeztu - International journal of cardiology, 2016 - Elsevier
Objectives The heart is frequently affected in neuromuscular disorders (NMDs). Some of
these patients even experience sudden cardiac death (SCD). In the following review, we …

Sudden cardiac death in neuromuscolar disorders: time to establish shared protocols for cardiac pacing

V Russo, A Rago, G Nigro - International …, 2016 - internationaljournalofcardiology.com
We read with interest the recent review about sudden cardiac death (SCD) in neuromuscular
disorders (NMD) by Finsterer et al.[1] which summarizes recent findings concerning …

[HTML][HTML] Heart disease in disorders of muscle, neuromuscular transmission, and the nerves

J Finsterer, C Stöllberger - Korean circulation journal, 2016 - ncbi.nlm.nih.gov
Little is known regarding cardiac involvement (CI) by neuromuscular disorders (NMDs). The
purpose of this review is to summarise and discuss the major findings concerning the types …

Cardiac involvement in the muscular dystrophies

NJ Silvestri, H Ismail, P Zimetbaum… - Muscle & …, 2018 - Wiley Online Library
Cardiac disease is a common clinical manifestation present in a variety of neuromuscular
disorders, most notably the muscular dystrophies. Heart disease may produce the …

Management of cardiac involvement associated with neuromuscular diseases: a scientific statement from the American Heart Association

B Feingold, WT Mahle, S Auerbach, P Clemens… - Circulation, 2017 - Am Heart Assoc
For many neuromuscular diseases (NMDs), cardiac disease represents a major cause of
morbidity and mortality. The management of cardiac disease in NMDs is made challenging …

[PDF][PDF] Subclinical cardiac involvement present as electrocardiographic abnormalities in various neuromuscular diseases

N Xiong, W Liu, J Li, S Luo, W Gu, W Zhu, J Xi, J Lin… - Heliyon, 2023 - cell.com
Background Cardiac involvement is commonly present in various neuromuscular diseases
which may develop life-threatening consequences. The early manifestation is often …

2022 HRS expert consensus statement on evaluation and management of arrhythmic risk in neuromuscular disorders

WJ Groh, D Bhakta, GF Tomaselli, RG Aleong… - Heart rhythm, 2022 - Elsevier
This international multidisciplinary document is intended to guide electrophysiologists,
cardiologists, other clinicians, and health care professionals in caring for patients with …

Clinical, genetic, and cardiac magnetic resonance imaging findings in primary desminopathies

K Strach, T Sommer, C Grohé, C Meyer, D Fischer… - Neuromuscular …, 2008 - Elsevier
We report the clinical, genetic and cardiac magnetic resonance imaging (MRI) findings in 11
German patients with heterozygous E245D, D339Y, R350P and L377P desmin mutations …

Cardiac involvement in muscular dystrophy: advances in diagnosis and therapy

A Yilmaz, U Sechtem - Heart, 2012 - heart.bmj.com
The term muscular dystrophy (MD) comprises various neuromuscular disorders that are
characterised by progressive muscle weakness affecting certain muscle groups, which are …

Electrocardiographic abnormalities and arrhythmias are strongly associated with the development of cardiomyopathy in muscular dystrophy

AM Shah, JL Jefferies, JW Rossano, JA Decker… - Heart Rhythm, 2010 - Elsevier
BACKGROUND: Dilated cardiomyopathy (DCM) is a well-recognized sequela of muscular
dystrophy (MD). Early identification of cardiac involvement with timely therapy can favorably …