Polycystic liver disease: pathophysiology, diagnosis and treatment

LF Norcia, EM Watanabe… - Hepatic Medicine …, 2022 - Taylor & Francis
Polycystic liver disease (PLD) is a clinical condition characterized by the presence of more
than 10 cysts in the liver. It is a rare disease Of genetic etiology that presents as an isolated …

[HTML][HTML] Polycystic liver disease: classification, diagnosis, treatment process, and clinical management

ZY Zhang, ZM Wang, Y Huang - World journal of hepatology, 2020 - ncbi.nlm.nih.gov
Polycystic liver disease (PLD) is a rare hereditary disease that independently exists in
isolated PLD, or as an accompanying symptom of autosomal dominant polycystic kidney …

Diagnosis and management of polycystic liver disease

TJG Gevers, JPH Drenth - Nature reviews Gastroenterology & …, 2013 - nature.com
Polycystic liver disease (PLD) is arbitrarily defined as a liver that contains> 20 cysts. The
condition is associated with two genetically distinct diseases: as a primary phenotype in …

Polycystic liver disease: an overview of pathogenesis, clinical manifestations and management

WR Cnossen, JPH Drenth - Orphanet journal of rare diseases, 2014 - Springer
Polycystic liver disease (PLD) is the result of embryonic ductal plate malformation of the
intrahepatic biliary tree. The phenotype consists of numerous cysts spread throughout the …

[HTML][HTML] Polycystic liver disease: a clinical review

N Chandok - Annals of hepatology, 2012 - Elsevier
Polycystic liver disease rarely occurs in isolation as part of autosomal dominant polycystic
liver disease, but more commonly, it exists as an extra-renal manifestation of autosomal …

[HTML][HTML] Pathophysiology, epidemiology, classification and treatment options for polycystic liver diseases

B Abu-Wasel, C Walsh, V Keough… - World Journal of …, 2013 - ncbi.nlm.nih.gov
Polycystic liver diseases (PLD) represent a group of genetic disorders in which cysts occur
in the liver (autosomal dominant polycystic liver disease) or in combination with cysts in the …

An update on the pathophysiology and management of polycystic liver disease

MYW Wong, GW McCaughan… - Expert Review of …, 2017 - Taylor & Francis
Introduction: Polycystic liver disease (PLD) is characterized by the presence of multiple
cholangiocyte-derived hepatic cysts that progressively replace liver tissue. They are …

Genetics, pathobiology and therapeutic opportunities of polycystic liver disease

P Olaizola, PM Rodrigues… - Nature Reviews …, 2022 - nature.com
Polycystic liver diseases (PLDs) are inherited genetic disorders characterized by
progressive development of intrahepatic, fluid-filled biliary cysts (more than ten), which …

Advances in management of polycystic liver disease

GT Everson, SM Helmke, B Doctor - Expert Review of …, 2008 - Taylor & Francis
The focus of this review is polycystic liver disease, a genetic disorder characterized by
multiple macroscopic liver cysts that initially bud from biliary epithelium but subsequently …

Systematic review: the pathophysiology and management of polycystic liver disease

F Temmerman, L Missiaen, B Bammens… - Alimentary …, 2011 - Wiley Online Library
Aliment Pharmacol Ther 2011; 34: 702–713 Summary Background Polycystic liver diseases
(PCLD) represent a group of genetic disorders in which cysts occur solely in the liver, or …