Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management

C McCarthy, N Gupta, SR Johnson, JY Jane… - The Lancet …, 2021 - thelancet.com
Lymphangioleiomyomatosis (LAM) is a slowly progressive, low-grade, metastasising
neoplasm of women, characterised by infiltration of the lung parenchyma with abnormal …

[HTML][HTML] Lymphangioleiomyomatosis—a wolf in sheep's clothing

EP Henske, FX McCormack - The Journal of clinical …, 2012 - Am Soc Clin Investig
Lymphangioleiomyomatosis (LAM) is a rare progressive lung disease of women. LAM is
caused by mutations in the tuberous sclerosis genes, resulting in activation of the mTOR …

Lymphangioleiomyomatosis: new concepts in pathogenesis, diagnosis, and treatment

R Meraj, KA Wikenheiser-Brokamp… - … in respiratory and …, 2012 - thieme-connect.com
Lymphangioleiomyomatosis (LAM) is a slowly progressive lung disease that is associated
with mutations in tuberous sclerosis complex genes, infiltration of the pulmonary …

Lymphangioleiomyomatosis: what do we know and what are we looking for?

S Harari, O Torre, J Moss - European Respiratory Review, 2011 - Eur Respiratory Soc
Lymphangioleiomyomatosis (LAM) is a rare disease characterised by proliferation of
abnormal smooth muscle-like cells (LAM cells) leading to progressive cystic destruction of …

Lymphangioleiomyomatosis

SR Johnson - Orphan lung diseases: a clinical guide to rare lung …, 2023 - Springer
Lymphangioleiomyomatosis (LAM) is a rare multisystem disease which predominantly
affects women. The disease occurs both sporadically and is common in women with …

Official American Thoracic Society/Japanese Respiratory Society clinical practice guidelines: lymphangioleiomyomatosis diagnosis and management

FX McCormack, N Gupta, GR Finlay… - American journal of …, 2016 - atsjournals.org
Background: Lymphangioleiomyomatosis (LAM) is a rare cystic lung disease that primarily
affects women. The purpose of these guidelines is to provide recommendations for the …

Lymphangioleiomyomatosis: a monogenic model of malignancy

VP Krymskaya, FX McCormack - Annual review of medicine, 2017 - annualreviews.org
Lymphangioleiomyomatosis (LAM) is a rare, low-grade, metastasizing neoplasm that arises
from an unknown source, spreads via the lymphatics, and targets the lungs. All pulmonary …

[HTML][HTML] Lymphangioleiomyomatosis: calling it what it is: a low-grade, destructive, metastasizing neoplasm

FX McCormack, WD Travis, TV Colby… - American journal of …, 2012 - atsjournals.org
Lymphangioleiomyomatosis (LAM) is a progressive cystic lung disease primarily affecting
women that has historically been classified and clinically managed as a nonneoplastic …

European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis

SR Johnson, JF Cordier, R Lazor… - European …, 2010 - Eur Respiratory Soc
METHODS The purpose of the LAM Task Force was to produce evidence based, consensus
guidelines for the diagnosis, assessment and treatment of patients with LAM. The two …

Clinical features, epidemiology, and therapy of lymphangioleiomyomatosis

AM Taveira-DaSilva, J Moss - Clinical epidemiology, 2015 - Taylor & Francis
Lymphangioleiomyomatosis (LAM) is a multisystem disease of women, characterized by
proliferation of abnormal smooth muscle-like LAM cells, leading to the formation of lung …