Case report: auditory neuropathy and central auditory processing deficits in a neuro-otological case-study of infratentorial superficial siderosis

N Kharytaniuk, P Cowley, DJ Werring… - Frontiers in …, 2021 - frontiersin.org
Hearing and balance impairment are the most frequently reported features of infratentorial
(classical) superficial siderosis (iSS). There are few comprehensive descriptions of …

Bilateral vestibulopathy in superficial siderosis

SY Lee, DH Lee, YJ Bae, JJ Song, JS Kim… - Frontiers in …, 2018 - frontiersin.org
Background: Superficial siderosis (SS) is a rare condition in which hemosiderin, an iron
storage complex, is deposited in neural tissues because of recurrent subarachnoid …

Superficial siderosis of the central nervous system: neurotological findings related to magnetic resonance imaging

F Wagner, M Buchwalder, R Wiest… - Otology & …, 2019 - journals.lww.com
Objective: To compare the neurotological results of five patients suffering from progressive
hearing loss and ataxia due to superficial siderosis (SS) with the magnetic resonance …

Superficial siderosis of the central nervous system: phenotype and implications for audiology and otology

SA Sydlowski, MJ Cevette, J Shallop - Otology & Neurotology, 2011 - journals.lww.com
Objective: Superficial siderosis of the central nervous system (SSCN) results after chronic
subarachnoid hemorrhage. Consequent demyelination, particularly of the cochleovestibular …

Vestibular dysfunction in patients with superficial siderosis of the central nervous system

T Takeda, Y Kawashima, C Hirai, A Makabe… - Otology & …, 2018 - journals.lww.com
Objective: To describe the vestibular function in patients with superficial siderosis of the
central nervous system (SSCN). Study Design: Retrospective analysis. Setting: Tertiary …

Superficial siderosis causing retrolabyrinthine involvement in both cochlear and vestibular branches of the eighth cranial nerve

M Ushio, S Iwasaki, K Sugasawa… - Acta oto …, 2006 - Taylor & Francis
Although superficial siderosis (SS) has been clinically characterized as a combination of
sensorineural hearing impairment, cerebellar ataxia and pyramidal signs, precise evaluation …

Health-Related Quality of Life in Adults With Classical Infratentorial Superficial Siderosis: A Cross-sectional Study

N Kharytaniuk, AA Mazaheri, M Pavlou, DJ Werring… - Neurology, 2022 - AAN Enterprises
Background and Objectives Infratentorial superficial siderosis (iSS) is a rare but disabling
neurologic condition characterized by progressive hearing loss and balance and mobility …

Bilateral vestibulopathy documented by video head impulse tests in superficial siderosis

KW Kang, C Lee, SH Kim, HH Cho… - Otology & …, 2015 - journals.lww.com
Objective: Superficial siderosis (SS) of the CNS is associated with cerebellar ataxia,
sensorineural hearing loss, and pyramidal symptoms, which result from iron depositions on …

Cochlear implantation in superficial siderosis

CS Kim, JJ Song, MH Park, Y Ho Kim… - Acta oto …, 2006 - Taylor & Francis
Superficial siderosis (SS) of the central nervous system has been thought to be a rare
condition that generates progressive hearing loss, ataxia, pyramidal signs, and dementia …

Olfactory dysfunction is common in classical infratentorial superficial siderosis of the central nervous system

N Kharytaniuk, EA Lim, E Chan, M Pavlou… - Journal of …, 2022 - Springer
Background Established features of classical infratentorial superficial siderosis (iSS) include
hearing loss, impaired balance, myelopathy and, less commonly, cognitive compromise …