[HTML][HTML] Mechanism-based strategies for the management of autoimmunity and immune dysregulation in primary immunodeficiencies

JE Walter, JR Farmer, Z Foldvari, TR Torgerson… - The Journal of Allergy …, 2016 - Elsevier
A broad spectrum of autoimmunity is now well described in patients with primary
immunodeficiencies (PIDs). Management of autoimmune disease in the background of PID …

Advances in the care of primary immunodeficiencies (PIDs): from birth to adulthood

N Mahlaoui, K Warnatz, A Jones, S Workman… - Journal of clinical …, 2017 - Springer
Primary immunodeficiencies (PIDs) are a widely heterogeneous group of inherited defects of
the immune system consisting of many clinical phenotypes with at least 300 underlying …

Autoimmunity in primary immunodeficiencies (PID)

GT Padron, VP Hernandez-Trujillo - Clinical Reviews in Allergy & …, 2023 - Springer
Primary immunodeficiency (PID) may impact any component of the immune system. The
number of PID and immune dysregulation disorders is growing steadily with advancing …

Autoimmunity and immune dysregulation in primary immune deficiency disorders

HK Lehman - Current allergy and asthma reports, 2015 - Springer
Primary immune deficiencies are often associated with autoimmune disease due to the
dysregulation of the immune system as a whole. In many immune deficiencies, lymphocytes …

[PDF][PDF] Primary immune regulatory disorders and targeted therapies

B Kolukısa, S Barış - Turkish Journal of Hematology, 2021 - jag.journalagent.com
Primary immune regulatory disorders (PIRDs) are a group of diseases belonging to inborn
errors of immunity. They usually exhibit lymphoproliferation, autoimmunities, and …

Autoimmunity in immunodeficiency

K Todoric, JB Koontz, D Mattox, TK Tarrant - Current allergy and asthma …, 2013 - Springer
Primary immunodeficiencies (PID) comprise a diverse group of clinical disorders with varied
genetic defects. Paradoxically, a substantial proportion of PID patients develop autoimmune …

Secondary immune deficiency and primary immune deficiency crossovers: hematological malignancies and autoimmune diseases

M Ballow, S Sánchez-Ramón, JE Walter - Frontiers in Immunology, 2022 - frontiersin.org
Primary immunodeficiencies (PIDs), a heterogenous group of inborn errors of immunity, are
predetermined at birth but may evolve with age, leading to a variable clinical and laboratory …

Primary immunodeficiencies unravel critical aspects of the pathophysiology of autoimmunity and of the genetics of autoimmune disease

A Coutinho, M Carneiro-Sampaio - Journal of clinical immunology, 2008 - Springer
Abstract Background Primary Immunodeficiencies (PIDs) represent unique opportunities to
understand the operation of the human immune system. Accordingly, PIDs associated with …

Patterns of immune dysregulation in primary immunodeficiencies: a systematic review

AA Mauracher, E Gujer, LM Bachmann… - The Journal of Allergy …, 2021 - Elsevier
Background Immune dysregulation is as important as susceptibility to infection in defining
primary immunodeficiencies (PIDs). Because of the variability and nonspecificity of the …

Autoimmune and inflammatory manifestations occur frequently in patients with primary immunodeficiencies

A Fischer, J Provot, JP Jais, A Alcais… - Journal of Allergy and …, 2017 - Elsevier
Background Primary immunodeficiencies (PIDs) are inherited diseases associated with a
considerable increase in susceptibility to infections. It is known that PIDs can also …