Pulmonary alveolar proteinosis: progress in the first 44 years
JF Seymour, JJ Presneill - … journal of respiratory and critical care …, 2002 - atsjournals.org
Pulmonary alveolar proteinosis is a rare clinical syndrome that was first described in 1958.
Subsequently, over 240 case reports and small series have described at least 410 cases in …
Subsequently, over 240 case reports and small series have described at least 410 cases in …
Hydrophobic surfactant proteins in lung function and disease
JA Whitsett, TE Weaver - New England Journal of Medicine, 2002 - Mass Medical Soc
Pulmonary surfactants consist of phospholipids and the hydrophobic proteins surfactant
protein B and surfactant protein C. These surfactants keep the alveoli in the lung open to the …
protein B and surfactant protein C. These surfactants keep the alveoli in the lung open to the …
Heterozygosity for a surfactant protein C gene mutation associated with usual interstitial pneumonitis and cellular nonspecific interstitial pneumonitis in one kindred
AQ Thomas, K Lane, J Phillips III, M Prince… - American journal of …, 2002 - atsjournals.org
Familial pulmonary fibrosis is a heterogeneous group of interstitial lung diseases of
unknown cause that is associated with multiple pathologic subsets. Mutations in the …
unknown cause that is associated with multiple pathologic subsets. Mutations in the …
Mutations in the surfactant protein C gene associated with interstitial lung disease
34 Rybicki BA, Maliarik MJ, Malvitz E, et al. The influence of T cell receptor and cytokine
genes on sarcoidosis susceptibility in African Americans. Hum Immunol 1999; 60: 867–874 …
genes on sarcoidosis susceptibility in African Americans. Hum Immunol 1999; 60: 867–874 …
Pulmonary interstitial glycogenosis: a new variant of neonatal interstitial lung disease
AM Canakis, E Cutz, D Manson… - American journal of …, 2002 - atsjournals.org
We present the clinical, radiologic, and pathologic findings in lung biopsies from seven
infants with atypical neonatal lung disease. All seven infants presented with tachypnea …
infants with atypical neonatal lung disease. All seven infants presented with tachypnea …
[PDF][PDF] Molecular mechanisms of pulmonary fibrosis
Introduction 3. Lessons from the inflammatory pathway 3.1. The paradigm of type 1 or type 2
cytokine network commitment 3.2. Chemokines 3.2. 1. Chemokines in inflammatory/fibrotic …
cytokine network commitment 3.2. Chemokines 3.2. 1. Chemokines in inflammatory/fibrotic …
Pediatric interstitial lung disease: children are not small adults
LL Fan, C Langston - American journal of respiratory and critical …, 2002 - atsjournals.org
Ichikado K, Honda O, Mihara N, Kozuka T, et al. Acute respiratory distress syndrome and
acute interstitial pneumonia: comparison of thin-section CT findings. J Comput Assist …
acute interstitial pneumonia: comparison of thin-section CT findings. J Comput Assist …
Involvement of cathepsin H in the processing of the hydrophobic surfactant-associated protein C in type II pneumocytes
F Brasch, A Ten Brinke, G Johnen, M Ochs… - American journal of …, 2002 - atsjournals.org
Surfactant protein C (SP-C) is synthesized by type II pneumocytes as a 21-kD propeptide
(proSP-C) which is proteolytically processed to a 4.2-kD dipalmitoylated protein. To …
(proSP-C) which is proteolytically processed to a 4.2-kD dipalmitoylated protein. To …
Lung surfactant in subacute pulmonary disease
G Devendra, RG Spragg - Respiratory research, 2002 - Springer
Pulmonary surfactant is a surface active material composed of both lipids and proteins that is
produced by alveolar type II pneumocytes. Abnormalities of surfactant in the immature lung …
produced by alveolar type II pneumocytes. Abnormalities of surfactant in the immature lung …
Component-specific surface and physiological activity in bovine-derived lung surfactants
RH Notter, Z Wang, EA Egan, BA Holm - Chemistry and Physics of Lipids, 2002 - Elsevier
Composition, surface activity and effects on pressure–volume (P–V) mechanics are
examined for lavaged calf lung surfactant (LS) and the clinical exogenous surfactants …
examined for lavaged calf lung surfactant (LS) and the clinical exogenous surfactants …