Inherited surfactant protein-B deficiency and surfactant protein-C associated disease: clinical features and evaluation
A Hamvas - Seminars in perinatology, 2006 - Elsevier
The pulmonary surfactant is a mixture of phospholipids and proteins synthesized, packaged,
and secreted by alveolar type II cells that lowers surface tension and prevents atelectasis at …
and secreted by alveolar type II cells that lowers surface tension and prevents atelectasis at …
Defects in surfactant synthesis: clinical implications
Neonatal respiratory distress syndrome is the most frequent respiratory cause of death and
morbidity in the first year of life in the United States [1–3]. Pulmonary morbidity in survivors of …
morbidity in the first year of life in the United States [1–3]. Pulmonary morbidity in survivors of …
Use of transgenic mice to study lung morphogenesis and function
JP Bridges, TE Weaver - ILAR journal, 2006 - academic.oup.com
Successful transition to air breathing at birth depends on perinatal maturation of the gas
exchange surface, resorption of fluid from the air spaces, and synthesis and secretion of …
exchange surface, resorption of fluid from the air spaces, and synthesis and secretion of …
Structure and influence on stability and activity of the N‐terminal propeptide part of lung surfactant protein C
J Li, E Liepinsh, A Almlén, J Thyberg… - The FEBS …, 2006 - Wiley Online Library
Mature lung surfactant protein C (SP‐C) corresponds to residues 24–58 of the 21 kDa proSP‐
C. A late processing intermediate, SP‐Ci, corresponding to residues 12–58 of proSP‐C …
C. A late processing intermediate, SP‐Ci, corresponding to residues 12–58 of proSP‐C …
[PDF][PDF] Korrektur der βc-defizienten Pulmonalen Alveolarproteinose (PAP) durch hämatopoetischen Stammzell-Gentransfer in einem βc-defizienten Mausmodell
V Kleff - 2006 - duepublico2.uni-due.de
Surfactant-Proteins zu gewährleisten und somit die Surfactanthomöostase aufrecht zu
erhalten [Berclaz et al., 2002a; Berclaz et al., 2002b; Bonfield et al., 2003; Shibata et al …
erhalten [Berclaz et al., 2002a; Berclaz et al., 2002b; Bonfield et al., 2003; Shibata et al …
[引用][C] Korrektur der βc-defizienten [Beta-c-defizienten] pulmonalen Alveolarproteinose (PAP) durch hämatopoetischen Stammzell-Gentransfer in einem βc …
V Kleff - 2006 - Duisburg, Essen, Univ., Diss., 2007