Alveolar surfactant homeostasis and the pathogenesis of pulmonary disease
JA Whitsett, SE Wert, TE Weaver - Annual review of medicine, 2010 - annualreviews.org
The alveolar region of the lung creates an extensive epithelial surface that mediates the
transfer of oxygen and carbon dioxide required for respiration after birth. Maintenance of …
transfer of oxygen and carbon dioxide required for respiration after birth. Maintenance of …
Genetic basis of children's interstitial lung disease
LM Nogee - Pediatric allergy, immunology, and pulmonology, 2010 - liebertpub.com
Specific genetic causes for children's interstitial lung disease (chILD) have been identified
within the past decade. These include deletions of or mutations in genes encoding proteins …
within the past decade. These include deletions of or mutations in genes encoding proteins …
Pulmonary alveolar proteinosis: an overview for internists and hospital physicians
M Das, GA Salzman - Hospital Practice, 2010 - Taylor & Francis
Pulmonary alveolar proteinosis (PAP) is a rare diffuse lung disease characterized by
abnormal accumulation of surfactant-associated phospholipoproteinaceous material in the …
abnormal accumulation of surfactant-associated phospholipoproteinaceous material in the …
Surfactant deficiency disorders: SP-B and ABCA3
LM Nogee - Molecular Basis of Pulmonary Disease: Insights from …, 2010 - Springer
Single gene disorders disrupting surfactant metabolism and resulting in acute and chronic
lung disease have been identified in recent years. This review focuses on lung disease …
lung disease have been identified in recent years. This review focuses on lung disease …
Eine Punktmutation in der 5'-flankierenden Region reduziert die Transkription des Surfactant Protein B (SP-B) Gens in H441-Zellen
P Meyn - 2010 - refubium.fu-berlin.de
Surfactant Protein B (SP-B) ist ein in Typ-II-Zellen der Lunge gebildetes 8 kDa schweres
Protein, das für die Funktion des Surfactants und damit für die Lungenfunktion äußerst …
Protein, das für die Funktion des Surfactants und damit für die Lungenfunktion äußerst …
Autoimmune Pulmonary Alveolar Proteinosis
BC Trapnell, K Nakata, Y Inoue - … of Pulmonary Disease: Insights from Rare …, 2010 - Springer
Pulmonary alveolar proteinosis (PAP) is a rare syndrome characterized by accumulation of
surfactant lipids and proteins in pulmonary alveoli that can result in progressive impairment …
surfactant lipids and proteins in pulmonary alveoli that can result in progressive impairment …