Emerging evidence for endoplasmic reticulum stress in the pathogenesis of idiopathic pulmonary fibrosis

H Tanjore, TS Blackwell… - American Journal of …, 2012 - journals.physiology.org
While the factors that regulate the onset and progression of idiopathic pulmonary fibrosis
(IPF) are incompletely understood, recent investigations have revealed that endoplasmic …

EMT and interstitial lung disease: a mysterious relationship

H Kage, Z Borok - Current opinion in pulmonary medicine, 2012 - journals.lww.com
Advances have been made in elucidating causes and mechanisms of EMT, potentially
leading to new treatment options, although contributions of EMT to lung fibrosis in vivo …

The pathogenesis of COPD and IPF: distinct horns of the same devil?

M Chilosi, V Poletti, A Rossi - Respiratory research, 2012 - Springer
New paradigms have been recently proposed in the pathogenesis of both chronic
obstructive pulmonary disease (COPD) and idiopathic pulmonary fibrosis (IPF), evidencing …

Unravelling the progressive pathophysiology of idiopathic pulmonary fibrosis

A Günther, M Korfei, P Mahavadi… - European …, 2012 - Eur Respiratory Soc
Idiopathic pulmonary fibrosis (IPF) is a life-threatening condition, with a median survival of<
3 yrs. The pathophysiology is not fully understood, but chronic injury of alveolar epithelial …

High-resolution structure of a BRICHOS domain and its implications for anti-amyloid chaperone activity on lung surfactant protein C

H Willander, G Askarieh, M Landreh… - Proceedings of the …, 2012 - National Acad Sciences
BRICHOS domains are encoded in> 30 human genes, which are associated with cancer,
neurodegeneration, and interstitial lung disease (ILD). The BRICHOS domain from lung …

Peripheral blood biomarkers in idiopathic pulmonary fibrosis

R Vij, I Noth - Translational Research, 2012 - Elsevier
In this article, we review the evidence for peripheral blood biomarkers in idiopathic
pulmonary fibrosis (IPF), a life-threatening fibrotic lung disease of unknown etiology. We …

Activin-A overexpression in the murine lung causes pathology that simulates acute respiratory distress syndrome

E Apostolou, A Stavropoulos… - American journal of …, 2012 - atsjournals.org
Rationale: Activin-A is up-regulated in various respiratory disorders. However, its precise
role in pulmonary pathophysiology has not been adequately substantiated in vivo …

The genetic and environmental causes of pulmonary fibrosis

K Macneal, DA Schwartz - Proceedings of the American Thoracic …, 2012 - atsjournals.org
Although substantial progress has been made in understanding the clinical, radiological,
and pathological manifestations of fibrosing interstitial lung diseases (ILD), it remains difficult …

Multiple ways to die: delineation of the unfolded protein response and apoptosis induced by surfactant protein C BRICHOS mutants

JA Maguire, S Mulugeta, MF Beers - … journal of biochemistry & cell biology, 2012 - Elsevier
Epithelial cell dysfunction is now recognized as an important mechanism in the
pathogenesis of interstitial lung diseases. Surfactant Protein C (SP-C), an alveolar type II cell …

Genetic interstitial lung disease

MS Devine, CK Garcia - Clinics in chest medicine, 2012 - chestmed.theclinics.com
The interstitial lung diseases (ILDs), or diffuse parenchymal lung diseases, are a
heterogeneous collection of more than 100 different pulmonary disorders that affect the …