Background: There is growing recognition and understanding of the entities that cause
interstitial lung disease (ILD) in infants. These entities are distinct from those that cause ILD …

Pulmonary surfactant is essential for life and is composed of a complex lipoprotein-like
mixture that lines the inner surface of the lung to prevent alveolar collapse at the end of …

Background Mutations in the gene encoding surfactant protein C (SP‐C) cause familial and
sporadic interstitial lung disease (ILD), which is associated with considerable morbidity and …

Over 35 years ago, Wanda Haschek and Hanspeter Witschi published a theory for the
pathogenesis of lung fibrosis that dared to challenge the longstanding view of lung fibrosis …

В обзоре на основании данных современной литературы представлены сведения о
биологии, физиологии и метаболизме сурфактанта, идентифицированных в …

Recent studies have suggested that some cases of familial interstitial pneumonia are
associated with mutations in the gene encoding surfactant protein C (SFTPC). We report …

Idiopathic pulmonary fibrosis (IPF) is a devastating, age-related lung disease of unknown
cause that has few treatment options. Once thought to be a chronic inflammatory process …

Abstract Over 35 years ago, Wanda Haschek and Hanspeter Witschi published a theory for
the pathogenesis of lung fibrosis that dared to challenge the longstanding view of lung …

Özet Amaç: Çocukluk çağındaki interstisyel akciğer hastalıkları nadir görüldüğünden ve
geniş bir yelpazeye sahip olduğundan, halen terimler, sınıflandırma, tedavi ve izlemleri …

Aim: There is not an exact consensus about the terminology, classification, therapy and
follow up of childhood interstitial lung diseases (ILD) because of its rarity and wide clinical …