In the last three decades, improvements in respiratory management are responsible for
increasing survival and improving quality of life for amyotrophic lateral sclerosis (ALS) …

NIV is an important adjunct to medications for patients with intractable dyspnea. Future
research should attempt to clarify the effectiveness of NIV at controlling dyspnea within and …

Non-invasive ventilation (NIV) increases survival and quality of life in motor neuron disease
(MND). NIV implementation historically occurred during a multi-day inpatient admission at …

Key points Amyotrophic Lateral Sclerosis (ALS) is the most common motor neuron disease
in adults. Its incidence in France is estimated at 2.5 per 100,000 population and its …

Objectives We retrospectively evaluated the decision-making process of amyotrophic lateral
sclerosis (ALS) patients on noninvasive positive pressure ventilation (NPPV) concerning …

Objective We performed a longitudinal study to elucidate the correlation between respiratory
insufficiency and respiratory biomarkers, including diaphragmatic compound muscle action …

Die durch die systematische Recherche identifizierte Literatur wurde mit der für das
jeweilige Studiendesign (systematische Reviews, Metaanalysen, RCTs und diagnostische …

The care of a person with ALS at the end of life will need particular attention and careful
management. As death approaches for a person with ALS it essential that the person with …

Progressive loss of function of the respiratory muscles ultimately results in respiratory failure,
the cause of death in the majority of ALS patients. However, before the strength of the …

Patients affected by glycogenosis type II frequently present sleepdisordered breathing. The
presence of symptoms suggestive of sleep breathing disorders was investigated, by a …