Childhood interstitial lung disease (chILD) comprises a large and heterogeneous group of
rare disorders characterized by diffuse pulmonary infiltrates, restrictive lung physiology, and …

Idiopathic pulmonary fibrosis (IPF) is a specific form of chronic interstitial lung pneumonia
associated with the histologic pattern of usual interstitial pneumonia (UIP). Although UIP is a …

Diffuse lung diseases in children, also called children's interstitial lung disease, are a
diverse group of rare disorders that cause disturbances of gas exchange in the lungs …

Lung disease affects more than 600 million people worldwide. While some of these lung
diseases have an obvious developmental component, there is growing appreciation that …

Pulmonary surfactant is a highly surface-active mixture of proteins and lipids that is
synthesized and secreted in the alveoli by type II epithelial cells and is found in the fluid …

Background Rare mutations in surfactant-associated genes contribute to neonatal
respiratory distress syndrome. The frequency of mutations in these genes in the Chinese …

肺表面活性物质蛋白B,C 基因变异与蒙古族早产儿呼吸窘迫综合征相关性研究 Page 1 临床儿科
杂志第34 卷第9 期2016 年9 月J Clin Pediatr Vol.34 No.9 Sep. 2016 · 645 · doi:10.3969/j.issn.1000-3606.2016.09.002 …

Idiopathic pulmonary fibrosis (IPF) is a distinct clinical syndrome of unknowncause
characterized by progressive dyspnea, dry cough, basilar crackles, arestrictive ventilatory …

Abstract The activation of Endoplasmic Reticulum (ER) stress and Unfolded Protein
Response (UPR) was first observed in patients with familial interstitial pneumonia (FIP) …