MR imaging in spinocerebellar ataxias: a systematic review
A Klaes, E Reckziegel, MC Franca… - American Journal …, 2016 - Am Soc Neuroradiology
BACKGROUND AND PURPOSE: Polyglutamine expansion spinocerebellar ataxias are
autosomal dominant slowly progressive neurodegenerative diseases with no current …
autosomal dominant slowly progressive neurodegenerative diseases with no current …
A longitudinal investigation into cognition and disease progression in spinocerebellar ataxia types 1, 2, 3, 6, and 7
A Moriarty, A Cook, H Hunt, ME Adams… - Orphanet Journal of …, 2016 - Springer
Background The natural history of clinical symptoms in the spinocerebellar ataxias (SCA) s
has been well characterised. However there is little longitudinal data comparing cognitive …
has been well characterised. However there is little longitudinal data comparing cognitive …
Cerebral and cerebellar grey matter atrophy in Friedreich ataxia: the IMAGE-FRDA study
Friedreich ataxia (FRDA) is traditionally associated with neuropathology in the cerebellar
dentate nucleus and spinal cord. Growing evidence also suggests involvement of the …
dentate nucleus and spinal cord. Growing evidence also suggests involvement of the …
MRI-based cerebellar volume measurements correlate with the International Cooperative Ataxia Rating Scale score in patients with spinocerebellar degeneration or …
D Hara, F Maki, S Tanaka, R Sasaki, Y Hasegawa - Cerebellum & Ataxias, 2016 - Springer
Background Progression of clinical symptoms and cerebellar atrophy may vary among
subtypes of spinocerebellar degeneration and multiple system atrophy. The aim of this cross …
subtypes of spinocerebellar degeneration and multiple system atrophy. The aim of this cross …
Cognitive deficits correlate with white matter deterioration in spinocerebellar ataxia type 2
CR Hernandez-Castillo, I Vaca-Palomares… - Journal of the …, 2016 - cambridge.org
Objectives: The aim of this study was to explore the relationship between cognitive and
white matter deterioration in a group of participants with spinocerebellar ataxia type 2 …
white matter deterioration in a group of participants with spinocerebellar ataxia type 2 …
Ataxia severity correlates with white matter degeneration in spinocerebellar ataxia type 7
CR Hernandez-Castillo… - American Journal …, 2016 - Am Soc Neuroradiology
BACKGROUND AND PURPOSE: There is a scarcity of information on the effect of white
matter degeneration in patients with spinocerebellar ataxia type 7. Therefore, we …
matter degeneration in patients with spinocerebellar ataxia type 7. Therefore, we …
MRI-based annual cerebellar volume atrophy rate as a biomarker of disease progression in patients with cerebellar degeneration
S Tanaka, F Maki, D Hara, R Sasaki… - Journal of St. Marianna …, 2016 - jstage.jst.go.jp
Purpose: We determined the annual cerebellar volume atrophy rate with magnetic
resonance imaging (MRI) and disease progression in ataxia with the International …
resonance imaging (MRI) and disease progression in ataxia with the International …