Large multicenter clinical trials have led to two recently approved drugs for patients with
idiopathic pulmonary fibrosis (IPF); yet, both of these therapies only slow disease …

Amyloid fibrils are physiologically insoluble biophysically specific β-sheet rich structures
formed by the aggregation of misfolded proteins. In vivo tissue amyloid formation is …

Although our understanding of the genetics and pathology of congenital lung diseases such
as surfactant protein deficiency, cystic fibrosis, and alpha-1 antitrypsin deficiency is …

Summary Mutations of the Surfactant Protein C (SPC) gene (SFTPC) have been associated
with childhood interstitial lung disease (chILD) with variable age of onset, severity of lung …

Alveolar epithelial type II (AEII) cells are “professional” secretory cells that synthesize and
secrete massive quantities of proteins to produce pulmonary surfactant and maintain airway …

Pulmonary surfactant (PS) reduces surface tension at the air-liquid interface in the alveolar
epithelium of the lung, which is required for breathing and for the pulmonary maturity of the …

В настоящее время активно ведутся научно-исследовательские работы по выявлению
генетических факторов риска развития бронхолегочной дисплазии (БЛД) у …

Epithelial cell dysfunction and abnormal wound healing have reemerged as central
concepts in the pathophysiology of a variety of parenchymal diseases of the distal adult lung …

Background: This study aims to evaluate the significance of whole lung lavage on prelavage
and postlavage blood gas analysis values of patients with pulmonary alveolar proteinosis …

PULMONAR PEDIÁTRICO: revisão de literatura. 2017. 43 f. Monografia (Aprimoramento)–
Hospital das Clínicas da Faculdade de Medicina de Ribeirão Preto da Universidade de São …