[HTML][HTML] ECFS best practice guidelines: the 2018 revision
C Castellani, AJA Duff, SC Bell, HGM Heijerman… - Journal of cystic …, 2018 - Elsevier
Developments in managing CF continue to drive dramatic improvements in survival. As
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …
Inflammation in cystic fibrosis: An update
EA Roesch, DP Nichols, JF Chmiel - Pediatric pulmonology, 2018 - Wiley Online Library
Inflammation plays a critical role in cystic fibrosis (CF) lung pathology and disease
progression making it an active area of research and important therapeutic target. In this …
progression making it an active area of research and important therapeutic target. In this …
Antimicrobial activity of ibuprofen against cystic fibrosis-associated gram-negative pathogens
PN Shah, KR Marshall-Batty, JA Smolen… - Antimicrobial agents …, 2018 - Am Soc Microbiol
Clinical trials have demonstrated the benefits of ibuprofen therapy in cystic fibrosis (CF)
patients, an effect that is currently attributed to ibuprofen's anti-inflammatory properties. Yet …
patients, an effect that is currently attributed to ibuprofen's anti-inflammatory properties. Yet …
The EGFR‐ADAM17 axis in chronic obstructive pulmonary disease and cystic fibrosis lung pathology
M Stolarczyk, BJ Scholte - Mediators of inflammation, 2018 - Wiley Online Library
Chronic obstructive pulmonary disease (COPD) and cystic fibrosis (CF) share molecular
mechanisms that cause the pathological symptoms they have in common. Here, we review …
mechanisms that cause the pathological symptoms they have in common. Here, we review …
[HTML][HTML] Interval estimation of the overall treatment effect in a meta-analysis of a few small studies with zero events
When a meta-analysis consists of a few small trials that report zero events, accounting for
heterogeneity in the (interval) estimation of the overall effect is challenging. Typically, we …
heterogeneity in the (interval) estimation of the overall effect is challenging. Typically, we …
S3-Leitlinie: Lungenerkrankung bei Mukoviszidose–Modul 2: Diagnostik und Therapie bei der chronischen Infektion mit Pseudomonas aeruginosa
C Schwarz, B Schulte-Hubbert, J Bend… - …, 2018 - thieme-connect.com
Mukoviszidose (Cystic Fibrosis, CF) ist die häufigste, autosomal-rezessiv vererbte
Multisystemerkrankung. In Deutschland sind ca. 8000 Menschen betroffen. Die Erkrankung …
Multisystemerkrankung. In Deutschland sind ca. 8000 Menschen betroffen. Die Erkrankung …
Is there a role for inhaled anti-inflammatory drugs in cystic fibrosis treatment?
Introduction: Cystic fibrosis (CF) is a congenital life-limiting, orphan disease affecting 1/2500–
1/3000 people worldwide with the greatest prevalence in Europe, North America and …
1/3000 people worldwide with the greatest prevalence in Europe, North America and …
[HTML][HTML] Strategies to prevent kidney injury from antibiotics in people with cystic fibrosis
N Ditchfield, FJ Gilchrist, SJ Davies… - The Cochrane Database …, 2018 - ncbi.nlm.nih.gov
Objectives This is a protocol for a Cochrane Review (intervention). The objectives are as
follows: To assess the benefits and harms of strategies (such as altering the type and dose …
follows: To assess the benefits and harms of strategies (such as altering the type and dose …
Strategies to prevent kidney injury from antibiotics in individuals with cystic fibrosis
N Ditchfield - 2018 - keele-repository.worktribe.com
Kidney damage in cystic fibrosis (CF) patients is most commonly caused by antibiotics, such
as aminoglycosides, which are used to treat Pseudomonas aeruginosa (PA). I conducted a …
as aminoglycosides, which are used to treat Pseudomonas aeruginosa (PA). I conducted a …
Ganglioside GM1 as adjuvant for Orkambi® therapy to restore plasma membrane stability and function of F508del-CFTR
G Mancini - 2018 - air.unimi.it
Cystic fibrosis (CF) is the most common, fatal genetic disease in the Caucasian population
caused by loss of function mutations in gene encoding for the cystic fibrosis transmembrane …
caused by loss of function mutations in gene encoding for the cystic fibrosis transmembrane …