[HTML][HTML] X-linked agammaglobulinemia (XLA): Phenotype, diagnosis, and therapeutic challenges around the world

ZA El-Sayed, I Abramova, JC Aldave, W Al-Herz… - World Allergy …, 2019 - Elsevier
Background X-linked agammaglobulinemia is an inherited immunodeficiency recognized
since 1952. In spite of seven decades of experience, there is still a limited understanding of …

A high prevalence of gastrointestinal manifestations in common variable immunodeficiency

S Pikkarainen, T Martelius, A Ristimäki… - Official journal of the …, 2019 - journals.lww.com
OBJECTIVES: Common variable immunodeficiency (CVID) is associated with a spectrum of
autoimmune complications. We studied the prevalence of gastrointestinal (GI) …

Comparison of common monogenic defects in a large predominantly antibody deficiency cohort

R Yazdani, H Abolhassani, F Kiaee, S Habibi… - The Journal of Allergy …, 2019 - Elsevier
Background Predominantly antibody deficiencies (PADs) are the most common primary
immunodeficiencies, characterized by hypogammaglobulinemia and inability to generate …

Comparison of clinical and immunological features and mortality in common variable immunodeficiency and agammaglobulinemia patients

Y Bagheri, A Vosughi, G Azizi, R Yazdani, N Hafezi… - Immunology letters, 2019 - Elsevier
Abstract Common Variable Immunodeficiency (CVID) and agammaglobulinemia are two of
the main types of symptomatic primary antibody deficiencies. The pathogenic origins of …

[PDF][PDF] Иммуноглобулин А (IgA): строение, рецепторы взаимодействия, селективный дефицит

МГ Шитикова - Иммунопатология, аллергология …, 2019 - immunopathology.com
Аннотация Основным иммуноглобулином, обеспечивающим иммунные гуморальные
реакции на поверхности слизистых оболочек, является иммуноглобулин А (IgA) …

Gastrointestinal manifestations in patients with common variable immunodeficiency

KJMR Al-Hussieni, SE Rasouli, G Azizi… - … and Genetics Journal, 2019 - igj.tums.ac.ir
Background/objectives: Common variable immunodeficiency (CVID) is one of the most
prevalent symptomatic primary immunodeficiencies (PIDs), which manifest a wide clinical …

Development A Guideline-based Decision Support System to Diagnosis of Primary Immunodeficiency Diseases

F Sepehri, M Langarizadeh, L Sharifi, G Azizi… - Frontiers in Health …, 2019 - ijmi.ir
Introduction: Primary immunodeficiency diseases (PID) are generally rare genetic disorders
affecting the immune system. Overlapping PIDs symptoms and signs is a challenge to …

[PDF][PDF] селективный дефицит

МГ Шитикова - Иммунопатология, аллергология, инфектология, 2019 - academia.edu
Аннотация Основным иммуноглобулином, обеспечивающим иммунные гуморальные
реакции на поверхности слизистых оболочек, является иммуноглобулин А (IgA) …

Cutaneous Infections in Immunocompromised Children

M Weinstein, H Ott, PH Hoeger - Harper's Textbook of Pediatric …, 2019 - Wiley Online Library
Patients with compromised immune systems are at particular risk for cutaneous infections.
Affected patients may exhibit either unusually severe or prolonged skin infections with …