Amyotrophic lateral sclerosis is a progressive and fatal neurodegenerative disease typically
presenting with bulbar or limb weakness. There is increasing evidence that amyotrophic …

Background: There has been no comprehensive longitudinal study of pulmonary functions
(PFTS) in ALS determining which measure is most sensitive to declines in respiratory …

Amyotrophic lateral sclerosis (ALS) is a multisystemic disease compromising both the
neuromuscular system and the cognitive status. Non-invasive ventilation (NIV) has been …

Motor neuron disease (MND) is a neurodegenerative disorder which leads to progressive
muscle weakness including respiratory muscle decline. The introduction of non-invasive …

Motor neuron disease or amyotrophic lateral sclerosis (ALS) is a rare, progressive, terminal
neurological disease that can strike anyone. As ALS progresses, respiratory muscle strength …

BACKGROUND: Obtaining benefits from long-term noninvasive ventilation (NIV) relies on
achieving adequate adherence to treatment. Reported adherence to NIV is variable and …

Objective In amyotrophic lateral sclerosis (ALS), early recognition of nocturnal
hypoventilation (NH) is essential to start noninvasive ventilation (NIV), but nocturnal …

L'altération de l'état nutritionnel lors de la Sclérose latérale amyotrophique (SLA) est liée à
une diminution des prises alimentaires et/ou une augmentation de la dépense énergétique …