Pathogenic variants in the genes affected in Alport syndrome (COL4A3–COL4A5) and their association with other kidney conditions: a review

J Savige, P Harraka - American Journal of Kidney Diseases, 2021 - Elsevier
Massively parallel sequencing identifies pathogenic variants in the genes affected in Alport
syndrome (COL4A3–COL4A5) in as many as 30% of individuals with focal and segmental …

[HTML][HTML] Consensus statement on standards and guidelines for the molecular diagnostics of Alport syndrome: refining the ACMG criteria

J Savige, H Storey, E Watson, JM Hertz… - European journal of …, 2021 - nature.com
Abstract The recent Chandos House meeting of the Alport Variant Collaborative extended
the indications for screening for pathogenic variants in the COL4A5, COL4A3 and COL4A4 …

[HTML][HTML] Molecular basis, diagnostic challenges and therapeutic approaches of alport syndrome: a primer for clinicians

R Martínez-Pulleiro, M García-Murias… - International journal of …, 2021 - mdpi.com
Alport syndrome is a genetic and hereditary disease, caused by mutations in the type IV
collagen genes COL4A3, COL4A4 and COL4A5, that affects the glomerular basement …

[HTML][HTML] Pathogenic LAMA5 variants and kidney disease

J Savige, P Harraka - Kidney360, 2021 - journals.lww.com
The manuscript by Nagano et al.(1) describes four children with the nephrotic syndrome and
biallelic pathogenic variants in LAMA5. Three of the children, each with two truncating …