West syndrome is an exceptional presentation of pyridoxine-and pyridoxal phosphate-dependent epilepsy: data from a French cohort and review of the literature

M Gibaud, M Barth, J Lefranc, K Mention… - Frontiers in …, 2021 - frontiersin.org
Objective: To characterize the electro-clinical presentation of patients with pyridoxine-
dependent epilepsy (PDE) and pyridoxal phosphate (PLP)-dependent epilepsy in order to …

Evaluation of the modified atkins diet for the treatment of epileptic spasms refractory to hormonal therapy: a randomized controlled trial

S Sharma, S Goel, D Kapoor, D Garg… - Journal of Child …, 2021 - journals.sagepub.com
Objectives: We aimed to evaluate the efficacy of the modified Atkins diet in children with
epileptic spasms who had failed hormonal therapy. Methods: Children aged 9 months to 3 …

Intravenous methylprednisolone versus oral prednisolone for west syndrome: a randomized open-label trial

D Kapoor, S Sharma, D Garg, S Samaddar… - Indian journal of …, 2021 - Springer
Objective To compare intravenous methylprednisolone (IVMP) with oral prednisolone (OP)
for the treatment of West syndrome. Methods In this randomized, open-label trial, children …

Long-term epilepsy control, motor function, cognition, sleep and quality of life in children with West syndrome

S Bhanudeep, P Madaan, N Sankhyan, L Saini… - Epilepsy Research, 2021 - Elsevier
Purpose To assess epilepsy, motor function, cognitive, sleep, and quality of life outcomes
and their predictors in a follow-up cohort with West syndrome (WS) at≥ 5 years of age …

Association of Child Neurology (AOCN)—Indian Epilepsy Society (IES) Consensus Guidelines for the Diagnosis and Management of West Syndrome

S Sharma, JS Kaushik, K Srivastava, JN Goswami… - Indian Pediatrics, 2021 - Springer
Justification West syndrome is one of the commonest causes of epilepsy in infants and
young children and is a significant contributor to neurodevelopmental morbidity. Multiple …

Dietary therapies for Epilepsy in low resource settings: challenges and successes

S Sharma - Journal of the International Child Neurology …, 2021 - jicna.org
Abstract The Ketogenic Diet (KD) is a high fat, low carbohydrate and restricted protein diet
which has been used for the treatment of drug resistant epilepsy in children. It is considered …

Clinical profile of children with West syndrome: a retrospective chart review

VK Gehlawat, V Arya, H Bhardwaj… - Journal of Family …, 2021 - journals.lww.com
Background: This study was intended to document the clinical profile and treatment outcome
of West syndrome in children attending a tertiary care centre in Northern India. Methods …

[HTML][HTML] Epileptic Encephalopathies in Infants and Children: Study of Clinico-Electroencephalographic Spectrum in a Tertiary Hospital in Bangladesh

B Debnath, RN Chowdhury, NC Shaha… - Open Journal of …, 2021 - scirp.org
Background: The epileptic encephalopathies collectively exact an immense personal,
medical, and financial toll on the affected children, their families, and the healthcare system …

Depression, Anxiety, and Parenting Stress among Mothers of Children with West Syndrome

P Kumar, V Arya, A Khanna, JS Kaushik - Indian Journal of Pediatrics, 2021 - Springer
The present cross-sectional study was designed to determine the prevalence of depression,
anxiety, and parenting stress in mothers of children aged 6 mo to 5 y with West syndrome …

The prognostic evaluation of West syndrome patients: A retrospective observational study

S Türay, F Hancı, M Dilek, N Kabakuş - Konuralp Medical Journal, 2021 - dergipark.org.tr
Objective: To determine neurodevelopmental and seizure prognoses in our patients with
West syndrome receiving adrenocorticotropic hormone (ACTH) therapy, and to identify the …