Abstract Purpose of Review: This review describes the most common motor neuron disease,
ALS. It discusses the diagnosis and evaluation of ALS and the current understanding of its …

BACKGROUND AND PURPOSE: Hirayama disease is a benign focal amyotrophy of the
distal upper limbs involving C7, C8, and T1 segmental myotomes with sparing of the …

Introduction Intraspinal cerebrospinal fluid (CSF) collection has been reported as a rare
cause of lower motor neuron (LMN) disorder. We report a case of bibrachial diplegia …

Objective Common symptoms in patients with a spinal CSF leak include orthostatic
headaches, neck stiffness, and hearing difficulties. The main outcome of this report was to …

Objective To evaluate the cervical spine alignment and range of motion (ROM) of neck
flexion in patients with Hirayama disease. Methods Fifty male patients were included, with …

Purpose Hirayama disease (HD) has been largely believed to affect only distal muscles.
However, the proximal upper extremities have been affected in some cases, which can be …

Our objective was to characterize the MR imaging features in a large and distinct series of
distal bimelic amyotrophy (DBMA) from India. We utilized a retrospective and prospective …

Discussion Three main hypotheses have been proposed for the pathophysiology of
amyotrophy of duropathy: 1) neurodegeneration caused by oxidative stress associated with …

METHODS: We conducted a retrospective cohort study including patients who presented
with a motor deficit of the upper limbs and an anterior interdural CSF collection on spinal …

Context: Ventral longitudinal intraspinal fluid collection (VLISFC) presenting as hand
amyotrophy has been described only in a few cases and there are no reports on associated …