Kasabach-Merritt phenomenon: classic presentation and management options

P Mahajan, J Margolin… - Clinical Medicine Insights …, 2017 - journals.sagepub.com
Kasabach-Merritt phenomenon (KMP) is a rare consumptive coagulopathy associated with
specific vascular tumors, kaposiform hemangioendothelioma, and tufted angioma …

[HTML][HTML] GNA14 somatic mutation causes congenital and sporadic vascular tumors by MAPK activation

YH Lim, A Bacchiocchi, J Qiu, R Straub… - The American Journal of …, 2016 - cell.com
Vascular tumors are among the most common neoplasms in infants and children; 5%–10%
of newborns present with or develop lesions within the first 3 months of life. Most are benign …

Kaposiform haemangioendothelioma of the head and neck

BLK Wong, VNY Lee, T Tikka, D Kim… - Critical Reviews in …, 2016 - Elsevier
Background Kaposiform haemangioendothelioma (KHE) is a tumor of intermediate
malignant potential derived from vascular endothelial cells. Due to rarity of head neck KHE …

Sirolimus therapy for kaposiform hemangioendothelioma with long‐term follow‐up

Z Wang, W Yao, H Sun, K Dong, Y Ma… - The Journal of …, 2019 - Wiley Online Library
Mammalian target of rapamycin inhibitors have shown promising results in the management
of kaposiform hemangioendothelioma (KHE). The purpose of this study was to present our …

Steroid‐resistant kaposiform hemangioendothelioma: a retrospective study of 37 patients treated with vincristine and long‐term follow‐up

Z Wang, K Li, W Yao, K Dong, X Xiao… - Pediatric Blood & …, 2015 - Wiley Online Library
Background Kaposiform hemangioendothelioma (KHE) with Kasabach–Merritt phenomenon
(KMP) still remains a particular and life‐threatening disease. The purpose of this study was …

Soft‐tissue tumours and tumour‐like conditions

E Calonje, KY Tsai - Rook's Textbook of Dermatology, Ninth …, 2016 - Wiley Online Library
In this chapter, most of the mesenchymal (soft‐tissue) tumours involving the skin (including
subcutaneous tissue) are described. Practically any soft‐tissue tumour can involve or …

Refractory Kasabach–Merritt phenomenon successfully treated with sirolimus, and a mini‐review of the published work

Z Wang, K Li, K Dong, X Xiao… - The Journal of …, 2015 - Wiley Online Library
Kasabach–Merritt phenomenon (KMP) is a rare and life‐threatening disease involving a
vascular tumor combined with severe consumptive coagulopathy. We present for the first …

Laryngomalacia and complicated, life-threatening mTOR-positive Kaposiform hemangioendothelioma cured by Supraglottoplasty and sirolimus

U Schroeder, M Lauten, G Stichtenoth… - Klinische …, 2014 - thieme-connect.com
The therapy of complicated Kaposiform hemangioendothelioma (KHE) is still difficult. We
present the first case of laryngomalacia with simultaneous mammalian target of Rapamycin …

Comparison of corticosteroid and vincristine in treating kaposiform hemangioendothelioma and tufted angioma: a systematic review and meta-analysis

W Yao, K Li, Z Wang, J Pei, X Liu… - European Journal of …, 2019 - thieme-connect.com
Objective To evaluate the outcome and safety of corticosteroids and vincristine (VCR) in the
treatment of kaposiform hemangioendothelioma (KHE) and tufted angioma (TA). Materials …

Up-to-date practical imaging evaluation of neonatal soft-tissue tumors: what radiologists need to know

R Restrepo, ML Francavilla, R Mas… - American Journal of …, 2017 - Am Roentgen Ray Soc
OBJECTIVE. The purposes of this article are to provide an up-to-date overview of neonatal
soft-tissue tumors, including information regarding their unique nature, and to present …