Genetics of congenital heart disease

K Williams, J Carson, C Lo - Biomolecules, 2019 - mdpi.com
Congenital heart disease (CHD) is one of the most common birth defects. Studies in animal
models and humans have indicated a genetic etiology for CHD. About 400 genes have been …

Cellular and engineered organoids for cardiovascular models

D Thomas, S Choi, C Alamana, KK Parker… - Circulation …, 2022 - Am Heart Assoc
An ensemble of in vitro cardiac tissue models has been developed over the past several
decades to aid our understanding of complex cardiovascular disorders using a reductionist …

[HTML][HTML] A transcription factor atlas of directed differentiation

J Joung, S Ma, T Tay, KR Geiger-Schuller… - Cell, 2023 - cell.com
Transcription factors (TFs) regulate gene programs, thereby controlling diverse cellular
processes and cell states. To comprehensively understand TFs and the programs they …

A patterned human primitive heart organoid model generated by pluripotent stem cell self-organization

B Volmert, A Kiselev, A Juhong, F Wang… - Nature …, 2023 - nature.com
Pluripotent stem cell-derived organoids can recapitulate significant features of organ
development in vitro. We hypothesized that creating human heart organoids by mimicking …

In vitro generation of functional murine heart organoids via FGF4 and extracellular matrix

J Lee, A Sutani, R Kaneko, J Takeuchi… - Nature …, 2020 - nature.com
Our understanding of the spatiotemporal regulation of cardiogenesis is hindered by the
difficulties in modeling this complex organ currently by in vitro models. Here we develop a …

Defining human cardiac transcription factor hierarchies using integrated single-cell heterogeneity analysis

JM Churko, P Garg, B Treutlein… - Nature …, 2018 - nature.com
Human induced pluripotent stem cell-derived cardiomyocytes (hiPSC-CMs) have become a
powerful tool for human disease modeling and therapeutic testing. However, their use …

Atrial‐like cardiomyocytes from human pluripotent stem cells are a robust preclinical model for assessing atrial‐selective pharmacology

HD Devalla, V Schwach, JW Ford, JT Milnes… - EMBO molecular …, 2015 - embopress.org
Drugs targeting atrial‐specific ion channels, Kv1. 5 or Kir3. 1/3.4, are being developed as
new therapeutic strategies for atrial fibrillation. However, current preclinical studies carried …

Atrial-like engineered heart tissue: an in vitro model of the human atrium

M Lemme, BM Ulmer, MD Lemoine, ATL Zech… - Stem cell reports, 2018 - cell.com
Cardiomyocytes (CMs) generated from human induced pluripotent stem cells (hiPSCs) are
under investigation for their suitability as human models in preclinical drug development …

[HTML][HTML] Transcriptomics-based network medicine approach identifies metformin as a repurposable drug for atrial fibrillation

JC Lal, C Mao, Y Zhou, SR Gore-Panter… - Cell Reports …, 2022 - cell.com
Effective drugs for atrial fibrillation (AF) are lacking, resulting in significant morbidity and
mortality. This study demonstrates that network proximity analysis of differentially expressed …

Impaired human cardiac cell development due to NOTCH1 deficiency

S Ye, C Wang, Z Xu, H Lin, X Wan, Y Yu… - Circulation …, 2023 - Am Heart Assoc
Background: NOTCH1 pathogenic variants are implicated in multiple types of congenital
heart defects including hypoplastic left heart syndrome, where the left ventricle is …