OCT angiography and evaluation of the choroid and choroidal vascular disorders

E Borrelli, D Sarraf, KB Freund, SR Sadda - Progress in retinal and eye …, 2018 - Elsevier
The recent introduction of optical coherence tomography angiography (OCTA) has
remarkably expanded our knowledge of the choroid through in vivo investigation of the …

Human cytochromes P450 in health and disease

DW Nebert, K Wikvall, WL Miller - … Transactions of the …, 2013 - royalsocietypublishing.org
There are 18 mammalian cytochrome P450 (CYP) families, which encode 57 genes in the
human genome. CYP2, CYP3 and CYP4 families contain far more genes than the other 15 …

Inherited retinal diseases: therapeutics, clinical trials and end points—a review

M Georgiou, K Fujinami… - Clinical & Experimental …, 2021 - Wiley Online Library
Inherited retinal diseases (IRDs) are a clinically and genetically heterogeneous group of
disorders characterised by photoreceptor degeneration or dysfunction. These disorders …

Retinitis pigmentosa

C Hamel - Orphanet journal of rare diseases, 2006 - Springer
Retinitis pigmentosa (RP) is an inherited retinal dystrophy caused by the loss of
photoreceptors and characterized by retinal pigment deposits visible on fundus examination …

[HTML][HTML] Dynamic lipid turnover in photoreceptors and retinal pigment epithelium throughout life

D Lewandowski, CL Sander, A Tworak, F Gao… - Progress in retinal and …, 2022 - Elsevier
The retinal pigment epithelium-photoreceptor interphase is renewed each day in a stunning
display of cellular interdependence. While photoreceptors use photosensitive pigments to …

Human cytochrome P450 enzymes

FP Guengerich - Cytochrome P450: structure, mechanism, and …, 2015 - Springer
Abstract The cytochrome P450 (P450) enzymes first attracted interest because of their
relevance to the metabolism of drugs, steroids, and carcinogens. Collectively, the 57 human …

Phenotyping and genotyping inherited retinal diseases: Molecular genetics, clinical and imaging features, and therapeutics of macular dystrophies, cone and cone-rod …

M Georgiou, AG Robson, K Fujinami… - Progress in retinal and …, 2024 - Elsevier
Inherited retinal diseases (IRD) are a leading cause of blindness in the working age
population and children. The scope of this review is to familiarise clinicians and scientists …

Next generation sequencing-based molecular diagnosis of retinitis pigmentosa: identification of a novel genotype-phenotype correlation and clinical refinements

F Wang, H Wang, HF Tuan, DH Nguyen, V Sun… - Human genetics, 2014 - Springer
Retinitis pigmentosa (RP) is a devastating form of retinal degeneration, with significant
social and professional consequences. Molecular genetic information is invaluable for an …

Gene variants associated with deep vein thrombosis

ID Bezemer, LA Bare, CJM Doggen, AR Arellano… - Jama, 2008 - jamanetwork.com
Context The genetic causes of deep vein thrombosis (DVT) are not fully understood.
Objective To identify single-nucleotide polymorphisms (SNPs) associated with DVT. Design …

Cytochrome P450 omega hydroxylase (CYP4) function in fatty acid metabolism and metabolic diseases

JP Hardwick - Biochemical pharmacology, 2008 - Elsevier
The cytochrome P450 gene 4 family (CYP4) consists of a group of over 63 members that ω-
hydroxylate the terminal carbon of fatty acids. In mammals, six subfamilies have been …