This Review provides an updated approach to the diagnosis of idiopathic pulmonary fibrosis
(IPF), based on a systematic search of the medical literature and the expert opinion of …

Pleuroparenchymal fibroelastosis (PPFE) is an unusual pulmonary disease with unique
clinical, radiological, and pathological characteristics. Designated a rare idiopathic …

Background: This document provides clinical recommendations for the diagnosis of
idiopathic pulmonary fibrosis (IPF). It represents a collaborative effort between the American …

Background: In 2002 the American Thoracic Society/European Respiratory Society
(ATS/ERS) classification of idiopathic interstitial pneumonias (IIPs) defined seven specific …

We previously described restrictive allograft syndrome as a form of chronic lung allograft
dysfunction, demonstrating restrictive pulmonary function decline. However, the …

In the updated American Thoracic Society–European Respiratory Society classification of
the idiopathic interstitial pneumonias (IIPs), the major entities have been preserved and …

Pleuroparenchymal fibroelastosis (PPFE) is a rare pulmonary fibrosis that is clinically
characterized by upperlobe predominant fibrosis. PPFE is a slowly progressive disorder and …

BACKGROUND Pleuroparenchymal fibroelastosis (PPFE) is a rare form of interstitial
pneumonia and sometimes coexists with a histologic usual interstitial pneumonia (UIP) …

Background Although the accurate diagnosis of pleuroparenchymal fibroelastosis (PPFE)
requires pathologic evaluation, this diagnosis is often suggested when the radiologic …

Background Physicians have few opportunities to perform surgical lung biopsy (SLB) to
diagnose idiopathic pleuroparenchymal fibroelastosis (IPPFE). Therefore, diagnostic criteria …