Disturbed lipid profile in common variable immunodeficiency–a pathogenic loop of inflammation and metabolic disturbances

SF Jorgensen, ME Macpherson… - Frontiers in …, 2023 - frontiersin.org
The relationship between metabolic and inflammatory pathways play a pathogenic role in
various cardiometabolic disorders and is potentially also involved in the pathogenesis of …

Inborn errors of immunity and related microbiome

R Hazime, FE Eddehbi, S El Mojadili… - Frontiers in …, 2022 - frontiersin.org
Inborn errors of immunity (IEI) are characterized by diverse clinical manifestations that are
dominated by atypical, recurrent, chronic, or severe infectious or non-infectious features …

Increased plasma levels of triglyceride-enriched lipoproteins associate with systemic inflammation, lipopolysaccharides, and gut dysbiosis in common variable …

ME Macpherson, T Skarpengland, JR Hov… - Journal of Clinical …, 2023 - Springer
Purpose Triglycerides (TG) and their major transport lipoprotein in the circulation (VLDL)
appear to be related to inflammation. Patients with common variable immunodeficiency …

Dysimmunity in common variable immunodeficiency is associated with alterations in oral, respiratory, and intestinal microbiota

MD Cabanero-Navalon, V Garcia-Bustos, A Mira… - Clinical …, 2023 - Elsevier
Common variable immunodeficiency (CVID) is the most common symptomatic primary
immunodeficiency characterized by decreased immunoglobulins and recurrent infections. Its …

Probiotic Limosilactobacillus reuteri DSM 17938 Changes Foxp3 Deficiency-Induced Dyslipidemia and Chronic Hepatitis in Mice

E Nessim Kostandy, JH Suh, X Tian, B Okeugo… - Nutrients, 2024 - mdpi.com
The probiotic Limosilactobacillus reuteri DSM 17938 produces anti-inflammatory effects in
scurfy (SF) mice, a model characterized by immune dysregulation, polyendocrinopathy …

Microbiome and Its Dysbiosis in Inborn Errors of Immunity

M Sharma, M Dhaliwal, R Tyagi, T Goyal, S Sharma… - Pathogens, 2023 - mdpi.com
Inborn errors of immunity (IEI) can present with infections, autoimmunity, lymphoproliferation,
granulomas, and malignancy. IEIs are due to genetic abnormalities that disrupt normal host …

Multi-omics analysis of naïve B cells of patients harboring the C104R mutation in TACI

N Ramirez, S Posadas-Cantera, N Langer… - Frontiers in …, 2022 - frontiersin.org
Common variable immunodeficiency (CVID) is the most prevalent form of symptomatic
primary immunodeficiency in humans. The genetic cause of CVID is still unknown in about …

[PDF][PDF] Enfermedad Pulmonar Intersticial Granulomatosa Linfocítica como modelo de disinmunidad

MJF Giner - 2023 - roderic.uv.es
3.1. Introducción a las Inmunodeficiencias Primarias……………………………………………...
29 3.2. Introducción a la Inmunodeficiencia Común Variable …

Inmunodeficiencia común variable y neoplasias: etiopatogenia del cáncer en el contexto de un error innato de la inmunidad

PB Silman - Revista Médica de la Universidad de Costa Rica, 2023 - revistas.ucr.ac.cr
Durante años se ha estudiado la relación entre el cáncer y las inmunodeficiencias
primarias, también llamadas errores innatos de la inmunidad. La inmunodeficiencia común …