Los registros de vida real han resultado fundamentales para el avance en el conocimiento
de numerosas enfermedades raras (ER), entre las que se encuentra la hipertensión arterial …

Pulmonary hypertension (PH) associated with chronic lung disease (CLD) is both common
and underrecognised. The presence of PH in the setting of lung disease has been …

Objectives To describe the clinical phenotype and prognosis of people in the Australian
Scleroderma (SSc) Cohort Study with pulmonary arterial hypertension (PAH) with or without …

Precapillary pulmonary hypertension (PH) is a significant complication of systemic sclerosis
(SSc). It represents one of the leading causes of morbidity and mortality, correlating with a …

Background Pulmonary involvement is the leading cause of death in systemic sclerosis
(SSc) and may manifest as interstitial lung disease (ILD), pulmonary arterial hypertension …

Aims We aimed to analyse the characteristics and in‐hospital outcomes of patients
hospitalized for heart failure (HF) with co‐morbid systemic sclerosis (SSc) and compare …

Systemic sclerosis (SSc) is a rare autoimmune disease in which interstitial lung disease
(ILD) is the leading cause of morbidity and mortality. Clinical management of the lung …

Objective The objective of this study was to identify those SSc patients with concurrent
pulmonary hypertension (PH)(SSc-PH patients) and interstitial lung disease (ILD) and …

Real-world registries have been critical to building the scientific knowledge of rare diseases,
including Pulmonary Arterial Hypertension (PAH). In the past 4 decades, a considerable …

Systemic sclerosis (SSc) is a complex autoimmune connective tissue disorder. SSc presents
with severe pathological clinical manifestations, including vasculature abnormalities …