Fontan-associated liver disease: screening, management, and transplant considerations

J Emamaullee, AN Zaidi, T Schiano, J Kahn… - Circulation, 2020 - Am Heart Assoc
Surgical innovation and multidisciplinary management have allowed children born with
univentricular physiology congenital heart disease to survive into adulthood. An estimated …

Chronic heart failure in congenital heart disease: a scientific statement from the American Heart Association

KK Stout, CS Broberg, WM Book, F Cecchin, JM Chen… - Circulation, 2016 - Am Heart Assoc
The past 60 years have brought remarkable advancements in the diagnosis and treatment of
congenital heart disease (CHD). Early diagnosis and improvements in cardiac surgery and …

2018 AHA/ACC guideline for the management of adults with congenital heart disease: a report of the American College of Cardiology/American Heart Association …

KK Stout, CJ Daniels, JA Aboulhosn, B Bozkurt… - Journal of the American …, 2019 - jacc.org
2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease: A
Report of the American College of Cardiology/American Heart Association Task Force on …

40-year follow-up after the Fontan operation: long-term outcomes of 1,052 patients

KN Pundi, JN Johnson, JA Dearani, KN Pundi… - Journal of the American …, 2015 - jacc.org
Background: There are limited long-term, single-cohort, follow-up studies available about
patients after the Fontan operation. Objectives: This study sought to determine the long-term …

Hepatic fibrosis is universal following Fontan operation, and severity is associated with time from surgery: a liver biopsy and hemodynamic study

DJ Goldberg, LF Surrey, AC Glatz… - Journal of the …, 2017 - Am Heart Assoc
Background Congestive hepatopathy is a recognized complication of Fontan physiology.
Data regarding the incidence of hepatopathy and risk factors are lacking. Methods and …

Diagnosis and management of noncardiac complications in adults with congenital heart disease: a scientific statement from the American Heart Association

GK Lui, A Saidi, AB Bhatt, LJ Burchill, JF Deen… - Circulation, 2017 - Am Heart Assoc
Life expectancy and quality of life for those born with congenital heart disease (CHD) have
greatly improved over the past 3 decades. While representing a great advance for these …

Congenital heart disease in the older adult: a scientific statement from the American Heart Association

AB Bhatt, E Foster, K Kuehl, J Alpert, S Brabeck… - Circulation, 2015 - Am Heart Assoc
what is presently known and to outline areas in which additional knowledge is critical to their
care. The focus of this scientific statement will be structural CHD, including coronary artery …

[HTML][HTML] The relentless effects of the Fontan paradox

J Rychik - Seminars in Thoracic and Cardiovascular Surgery …, 2016 - Elsevier
The Fontan operation is the anticipated palliative strategy for children born with single-
ventricle type of congenital heart disease. As a result of important circulatory limitations, a …

Failure of the fontan circulation

M Gewillig, DJ Goldberg - Heart failure clinics, 2014 - heartfailure.theclinics.com
A normal mammalian cardiovascular system consists of a double circuit, pulmonary and
systemic, connected in series and powered by a double pump. In the absence of congenital …

The clinical spectrum of Fontan-associated liver disease: results from a prospective multimodality screening cohort

ID Munsterman, AL Duijnhouwer… - European heart …, 2019 - academic.oup.com
Aims Liver fibrosis and cirrhosis are a consequence of a Fontan physiology, and determine
prognosis. It is unclear whether non-invasive assessment of liver pathology is helpful to …