Evaluation and management of the child and adult with Fontan circulation: a scientific statement from the American Heart Association

J Rychik, AM Atz, DS Celermajer, BJ Deal… - Circulation, 2019 - Am Heart Assoc
It has been 50 years since Francis Fontan pioneered the operation that today bears his
name. Initially designed for patients with tricuspid atresia, this procedure is now offered for a …

Energetics of blood flow in cardiovascular disease: concept and clinical implications of adverse energetics in patients with a Fontan circulation

FM Rijnberg, MG Hazekamp, JJ Wentzel… - Circulation, 2018 - Am Heart Assoc
Visualization and quantification of the adverse effects of distorted blood flow are important
emerging fields in cardiology. Abnormal blood flow patterns can be seen in various …

[PDF][PDF] Heterotaxy syndrome

SJ Kim - Korean circulation journal, 2011 - synapse.koreamed.org
Heterotaxy is defined as an abnormality where the internal thoraco-abdominal organs
demonstrate abnormal arrangement across the left-right axis of the body. This broad term …

Pulmonary arteriovenous malformations after the superior cavopulmonary shunt: mechanisms and clinical implications

MN Kavarana, JA Jones, RE Stroud… - Expert review of …, 2014 - Taylor & Francis
Children with functional single ventricle heart disease are commonly palliated down a
staged clinical pathway toward a Fontan completion procedure (total cavopulmonary …

[HTML][HTML] Pulmonary vascular sequelae of palliated single ventricle circulation: arteriovenous malformations and aortopulmonary collaterals

AD Spearman, S Ginde - Journal of Cardiovascular Development and …, 2022 - mdpi.com
Children and adults with single ventricle congenital heart disease (CHD) develop many
sequelae during staged surgical palliation. Universal pulmonary vascular sequelae in this …

[HTML][HTML] Cavopulmonary pathway modification in patients with heterotaxy and newly diagnosed or persistent pulmonary arteriovenous malformations after a modified …

DB McElhinney, GR Marx, AC Marshall… - The Journal of Thoracic …, 2011 - Elsevier
OBJECTIVE: Pulmonary arteriovenous malformations are an important but uncommon
complication of cavopulmonary connection, particularly in patients with heterotaxy. Absence …

Surgically corrected congenital heart disease: utility of 64-MDCT

PJ Spevak, PT Johnson… - American Journal of …, 2008 - Am Roentgen Ray Soc
OBJECTIVE. The purpose of this article is to review the CT appearance of postoperative
morphology and complications after surgical correction of congenital heart anomalies …

Inclusion of hepatic venous drainage in patients with pulmonary arteriovenous fistulas

SJ Kim, EJ Bae, JY Lee, HG Lim, C Lee… - The Annals of thoracic …, 2009 - Elsevier
BACKGROUND: It is well known that hepatic vein (HV) inclusion can ameliorate cyanosis in
patients with pulmonary arteriovenous fistulas (PAVFs) during the sequence of Fontan type …

Congenital portosystemic venous connections and other abdominal venous abnormalities in patients with polysplenia and functionally univentricular heart disease: a …

DB McElhinney, GR Marx… - Congenital Heart …, 2011 - Wiley Online Library
Objective. Published case reports suggest that congenital portosystemic venous
connections (PSVC) and other abdominal venous anomalies may be relatively frequent and …

Outcomes of the Kawashima: A Society of Thoracic Surgeons Congenital Heart Surgery Database Analysis

JR Miller, KD Hill, D Thibault, K Chiswell… - The Annals of Thoracic …, 2024 - Elsevier
Background We aimed to evaluate the effect of age at operation on postoperative outcomes
in children undergoing a Kawashima operation. Methods The Society of Thoracic Surgeons …