Common variable immunodeficiency: epidemiology, pathogenesis, clinical manifestations, diagnosis, classification, and management.

R Yazdani, S Habibi, L Sharifi, G Azizi… - … allergology & clinical …, 2019 - europepmc.org
Common variable immunodeficiency (CVID) is a heterogeneous disorder characterized by
hypogammaglobulinemia and increased susceptibility to recurrent bacterial infections. It is …

Organ‐based clues for diagnosis of inborn errors of immunity: A practical guide for clinicians

F Mohammadi, A Yadegar, M Mardani… - Immunity …, 2023 - Wiley Online Library
Inborn errors of immunity (IEI) comprise a group of about 490 genetic disorders that lead to
aberrant functioning or the development of distinct immune system components. So far, a …

Bone Mineral Density is Related to CD4+ T Cell Counts and Muscle Mass is Associated with B Cells in Common Variable Immunodeficiency Patients

DB de Melo, RMR Pereira, B Sini… - … Metabolic & Immune …, 2024 - ingentaconnect.com
Background: Common variable immunodeficiency (CVID) is a primary immunodeficiency
characterized by chronic/recurrent respiratory infections, bronchiectasis, autoimmunity …

Clinical features and predictors of osteoarticular manifestations in common variable immunodeficiency

M Ben Khaled, A Merdassi, S Rekaya, IB Fraj… - Clinical …, 2023 - Springer
Introduction This study aimed to assess osteoarticular manifestations in patients with
common variable immunodeficiency (CIVD) and to identify the predictive factors. Methods …

Gastrointestinal Involvement in Primary Antibody Deficiencies

T Milota, J Smetanova, I Klojdova - Gastrointestinal Disorders, 2023 - mdpi.com
Primary antibody deficiencies (PADs) are the most frequent group of inborn errors of
immunity. Impaired B-cell development, reduced production of immunoglobulins (mainly IgG …

Mannose-Binding Lectin Protein Deficiency Among Patients with Primary Immunodeficiency Disease Receiving IVIG Therapy

G Azizi, F Kiaee, S Yaslianifard… - … Metabolic & Immune …, 2018 - ingentaconnect.com
Background: Primary immunodeficiencies (PIDs) are inherited disorders in which one or
several components of the immune system are defective. Immunoglobulin replacement …

[PDF][PDF] Bone Metabolism Alterations in Patients with Common Variable Immune Deficiency: A Retrospective Cohort Study.

G Aytekin, F Çölkesen, E YILDIZ, Ş Arslan… - Asthma Allergy …, 2020 - researchgate.net
Objective: Common variable immunodeficiency (CVID) is a relatively frequent primary
immunodeficiency disorder characterized by impaired B cell differentiation with …

[引用][C] 自己免疫疾患におけるBTK 阻害剤チラブルチニブの薬理学的作用の研究

有座夕子 - 2019 - 北海道大学