Treatment strategies for GLILD in common variable immunodeficiency: a systematic review

OAC Lamers, BM Smits, HL Leavis, GJ de Bree… - Frontiers in …, 2021 - frontiersin.org
Introduction Besides recurrent infections, a proportion of patients with Common Variable
Immunodeficiency Disorders (CVID) may suffer from immune dysregulation such as …

COVID-19 in complex common variable immunodeficiency patients affected by lung diseases

C Milito, V Soccodato, S Auria… - Current Opinion in …, 2021 - journals.lww.com
COVID-19 in complex common variable immunodeficiency patient... : Current Opinion in Allergy
and Clinical Immunology COVID-19 in complex common variable immunodeficiency patients …

Bronchiectasis in primary antibody deficiencies: a multidisciplinary approach

LA Wall, EL Wisner, KS Gipson… - Frontiers in …, 2020 - frontiersin.org
Bronchiectasis, the presence of bronchial wall thickening with airway dilatation, is a
particularly challenging complication of primary antibody deficiencies. While susceptibility to …

Mortality in severe antibody deficiencies patients during the first two years of the COVID-19 pandemic: vaccination and monoclonal antibodies efficacy

C Milito, F Cinetto, A Palladino, G Garzi, A Punziano… - Biomedicines, 2022 - mdpi.com
Patients with severely impaired antibody responses represent a group at-risk in the SARS-
CoV-2 pandemic due to the lack of Spike-specific neutralizing antibodies. The main …

Progressive depletion of b and t lymphocytes in patients with ataxia telangiectasia: Results of the italian primary immunodeficiency network

E Cirillo, A Polizzi, A Soresina, R Prencipe… - Journal of Clinical …, 2022 - Springer
Ataxia telangiectasia (AT) is a rare neurodegenerative genetic disorder due to bi-allelic
mutations in the Ataxia Telangiectasia Mutated (ATM) gene. The aim of this paper is to better …

Consensus of the Italian Primary Immunodeficiency Network on transition management from pediatric to adult care in patients affected with childhood-onset inborn …

E Cirillo, G Giardino, S Ricci, V Moschese… - Journal of Allergy and …, 2020 - Elsevier
Medical advances have dramatically improved the long-term prognosis of children and
adolescents with inborn errors of immunity (IEIs). Transfer of the medical care of individuals …

Interstitial lung disease in primary immunodeficiency: towards a brighter future

JR Hurst, K Warnatz - European Respiratory Journal, 2020 - Eur Respiratory Soc
Lung disease is a frequent clinical manifestation in people living with primary
immunodeficiency diseases, the most prevalent of which are common variable …

[HTML][HTML] Sarcoidosis versus Granulomatous and Lymphocytic Interstitial Lung Disease in Common Variable Immunodeficiency: A Comparative Review

H Buso, C Discardi, P Bez, F Muscianisi, J Ceccato… - …, 2024 - ncbi.nlm.nih.gov
Abstract Sarcoidosis and Granulomatous and Lymphocytic Interstitial Lung Diseases
(GLILD) are two rare entities primarily characterised by the development of Interstitial Lung …

Non-infectious Pulmonary Complications in Children with Primary Immunodeficiency

W Mongkonsritragoon, R Srivastava… - Clinical Medicine …, 2023 - journals.sagepub.com
Primary immune deficiency (PID) is a large group of diseases characterized by defective
immune function, leading to recurrent infections, and immune dysregulation. Clinical …

Bronchiectasis and obstructive lung diseases in primary antibody deficiencies and beyond: update on management and pathomechanisms

LG Hanitsch - Current Opinion in Allergy and Clinical Immunology, 2022 - journals.lww.com
Management of PAD patients with chronic lung disease requires a multidisciplinary team
approach including immunology, pulmonology, infectious disease and physiotherapy …