The anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitides (AAV) are a
heterogeneous group of rare syndromes characterized by necrotizing inflammation of small …

Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) comprises
granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA) and eosinophilic …

Two antifibrotic medications (nintedanib and pirfenidone) were recommended
(conditionally) for the treatment of patients with idiopathic pulmonary fibrosis (IPF) in the …

Pulmonary complications in CTD are common and can involve the interstitium, airways,
pleura and pulmonary vasculature. ILD can occur in all CTD (CTD‐ILD), and may vary from …

Anti-neutrophil cytoplasmic antibodies (ANCA) vasculitides are immune-mediated disorders
that primarily affect small blood vessels of the airway and kidneys. Lung involvement, one of …

Lung involvement in connective tissue diseases is associated with substantial morbidity and
mortality, most commonly in the form of interstitial lung disease, and can occur in any of …

The respiratory manifestations of eosinophilic granulomatosis with polyangiitis (EGPA) have
not been studied in detail. In this retrospective multicentre study, EGPA was defined by …

Objective. To evaluate the clinical presentation and long-term outcome of a vasculitis centre
cohort of patients with microscopic polyangiitis (MPA) with respect to organ manifestations …

Antineutrophil cytoplasmic antibodies (ANCA)-associated vasculitis (AAV) is a group of
systemic vasculitides that predominantly affect small vessels, including granulomatosis with …

Lung involvement is one of the most common clinical features in ANCA-associated
vasculitides (AAV), including granulomatosis with polyangiitis (GPA), microscopic …