Context Rosai-Dorfman disease is an uncommon histiocytic disorder most frequently
presenting as bilateral cervical lymphadenopathy in children and young adults. Extranodal …

IgG4-related disease is a newly recognized fibro-inflammatory condition characterized by
several features: a tendency to form tumefactive lesions in multiple sites; a characteristic …

IgG4-related disease has been identified in various organs, but whether or not there are
organ-specific characteristics related to the etiologic factors is still unknown. Here, we …

IgG4-related systemic disease is an autoimmune disease that was first recognized in the
pancreas but also affects other organs. This disease may manifest as tubulointerstitial …

An elevated serum titer of immunoglobulin G4 (IgG4), the least common (3% to 6%) of the 4
subclasses of IgG, is a surrogate marker for the recently characterized IgG4-related …

IgG4-RSD is an underrecognized condition about which knowledge is now growing rapidly.
Yet there remain many unknowns with regard to its cause, pathogenesis, various clinical …

Abstract Immunoglobulin G4 (IgG4)-related disorders can occur in the respiratory system.
However, the clinicopathologic characteristics have not been well clarified. In this study, we …

Recognition of IgG4-related disease as an independent chronic inflammatory disorder is a
relatively new concept; previously, the condition was thought to represent a subtype of …

IgG4-related disease (IgG4-RD) is a systemic immune-mediated disease that typically
manifests as fibro-inflammatory masses that can affect nearly any organ system. Renal …

IgG4‐related diseases comprise a recently recognized systemic syndrome characterized by
mass‐forming lesions in mainly exocrine tissue that consist of lymphoplasmacytic infiltrates …