Expert consensus recommendations for the suspicion and diagnosis of transthyretin cardiac amyloidosis

MS Maurer, S Bokhari, T Damy, S Dorbala… - Circulation: Heart …, 2019 - Am Heart Assoc
Cardiomyopathy is a manifestation of transthyretin amyloidosis (ATTR), which is an
underrecognized systemic disease whereby the transthyretin protein misfolds to form fibrils …

ASNC/AHA/ASE/EANM/HFSA/ISA/SCMR/SNMMI expert consensus recommendations for multimodality imaging in cardiac amyloidosis: part 1 of 2—evidence base …

S Dorbala, Y Ando, S Bokhari, A Dispenzieri… - Journal of Nuclear …, 2019 - Springer
Cardiac amyloidosis is a form of restrictive infiltrative cardiomyopathy that confers significant
mortality. Due to the relative rarity of cardiac amyloidosis, clinical and diagnostic expertise in …

Systemic amyloidosis

AD Wechalekar, JD Gillmore, PN Hawkins - The Lancet, 2016 - thelancet.com
Tissue deposition of protein fibrils causes a group of rare diseases called systemic
amyloidoses. This Seminar focuses on changes in their epidemiology, the current approach …

How to image cardiac amyloidosis: a practical approach

S Dorbala, S Cuddy, RH Falk - Cardiovascular Imaging, 2020 - jacc.org
Cardiac amyloidosis (CA) is one of the most rapidly progressive forms of heart disease, with
a median survival from diagnosis, if untreated, ranging from< 6 months for light chain …

Cardiac amyloidosis: an update on pathophysiology, diagnosis, and treatment

OK Siddiqi, FL Ruberg - Trends in cardiovascular medicine, 2018 - Elsevier
The amyloidoses are a group of systemic diseases characterized by organ deposition of
misfolded protein fragments of diverse origins. The natural history of the disease …

Procedural recommendations of cardiac PET/CT imaging: standardization in inflammatory-, infective-, infiltrative-, and innervation (4Is)-related cardiovascular …

RHJA Slart, AWJM Glaudemans, O Gheysens… - European journal of …, 2021 - Springer
With this document, we provide a standard for PET/(diagnostic) CT imaging procedures in
cardiovascular diseases that are inflammatory, infective, infiltrative, or associated with …

Expert consensus on the monitoring of transthyretin amyloid cardiomyopathy

P Garcia‐Pavia, F Bengel, D Brito… - European journal of …, 2021 - Wiley Online Library
Transthyretin amyloid cardiomyopathy (ATTR‐CM) is a life‐threatening condition with a
heterogeneous clinical presentation. The recent availability of treatment for ATTR‐CM has …

Diagnosis and treatment of cardiac amyloidosis: position statement of the German Cardiac Society (DGK)

A Yilmaz, J Bauersachs, F Bengel, R Büchel… - Clinical Research in …, 2021 - Springer
Systemic forms of amyloidosis affecting the heart are mostly light-chain (AL) and
transthyretin (ATTR) amyloidoses. The latter is caused by deposition of misfolded …

Myocardial amyloidosis: the exemplar interstitial disease

M Fontana, A Ćorović, P Scully, JC Moon - JACC: Cardiovascular Imaging, 2019 - jacc.org
Cardiac involvement drives prognosis and treatment choices in cardiac amyloidosis.
Echocardiography is the first-line examination for patients presenting with heart failure, and …

Diagnostic imaging of cardiac amyloidosis

A Martinez-Naharro, AJ Baksi, PN Hawkins… - Nature Reviews …, 2020 - nature.com
Systemic amyloidosis encompasses a debilitating, under-diagnosed but increasingly
recognized group of disorders characterized by the extracellular deposition of misfolded …