Systemic sclerosis (SSc) is a systemic autoimmune disease that is characterised by
endothelial dysfunction resulting in a small-vessel vasculopathy, fibroblast dysfunction with …

Objective. To measure the prevalence of different types of pulmonary hypertension (PH) and
to identify patients with systemic sclerosis (SSc) at highest risk in a multicenter European …

CT scanning can also aid in identifying an aetiology of bronchiectasis eg Allergic
bronchopulmonary aspergillosis (ABPA), Non-tuberculous mycobacteria (NTM), primary …

Objective Earlier detection of pulmonary arterial hypertension (PAH), a leading cause of
death in systemic sclerosis (SSc), facilitates earlier treatment. The objective of this study was …

Objective Pulmonary arterial hypertension (PAH) affects up to 15% of patients with
connective tissue diseases (CTDs). Previous recommendations developed as part of larger …

Background Pulmonary hypertension (PHT) lacks community prevalence and outcome data.
Objective To characterise minimum 'indicative'prevalences and mortality data for all forms of …

Pulmonary arterial hypertension (PAH) is a dreaded complication of systemic sclerosis (SSc)
that occurs in∼ 10% of patients. Most individuals present with severe symptoms, significant …

Objective. The prevalence of organ complications in scleroderma (systemic sclerosis; SSc)
varies by definition used. This study was done to determine the frequency of several features …

Pulmonary arterial hypertension is a lethal complication of different connective tissue
diseases such as systemic sclerosis, mixed connective tissue disease and systemic lupus …

Background Pulmonary arterial hypertension (PAH) is the leading cause of death in
systemic sclerosis (SSc). Annual screening with echocardiogram (ECHO) is recommended …