Periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome: A review

A Wang, K Manthiram, F Dedeoglu… - World Journal of …, 2021 - mednexus.org
Periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome is the most
common periodic fever condition in children, with most cases appearing by the age of 5 …

PFAPA (periodic fever, aphthous stomatitis, pharyngitis, and adenitis) syndrome: an overview of genetic background

K Asna Ashari, N Rezaei - Clinical Rheumatology, 2021 - Springer
Periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome is
an autoinflammatory disorder with an uncertain origin. PFAPA manifestations occur in the …

Consensus treatment plans for new‐onset systemic juvenile idiopathic arthritis

EM Dewitt, Y Kimura, T Beukelman… - Arthritis care & …, 2012 - Wiley Online Library
Objective There is wide variation in therapeutic approaches to systemic juvenile idiopathic
arthritis (JIA) among North American rheumatologists. Understanding the comparative …

[HTML][HTML] Periodic fever, aphthous stomatitis, pharyngitis, and adenitis syndrome and syndrome of unexplained recurrent fevers in children and adults

J Hausmann, F Dedeoglu, L Broderick - The Journal of Allergy and Clinical …, 2023 - Elsevier
Children and adults with autoinflammatory disorders, who often experience recurrent fevers,
rashes, cold-induced symptoms, conjunctivitis, lymphadenopathy, recurrent infections …

[HTML][HTML] Colchicine effectiveness and safety in periodic fever, aphthous stomatitis, pharyngitis, and adenitis

T Welzel, M Ellinghaus, AL Wildermuth… - Frontiers in …, 2021 - frontiersin.org
Introduction: Periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA)
is the most common fever syndrome in childhood. High disease activity (DA) dramatically …

Systemic autoinflammatory diseases: a growing family of disorders of overlapping immune dysfunction

MJ Gutierrez, SK Lapidus - Rheumatic Disease Clinics, 2022 - rheumatic.theclinics.com
The first known systemic autoinflammatory disease (SAID), familial Mediterranean fever
(FMF), was described in 1945, 1 and the term, autoinflammatory, was coined in 1999 to …

[HTML][HTML] PFAPA syndrome: Clinical, laboratory and therapeutic features in a single-centre cohort

C Lazea, L Damian, R Vulturar… - International Journal of …, 2022 - ncbi.nlm.nih.gov
PFAPA Syndrome: Clinical, Laboratory and Therapeutic Features in a Single-Centre Cohort -
PMC Back to Top Skip to main content NIH NLM Logo Access keys NCBI Homepage MyNCBI …

Undifferentiated recurrent fevers in pediatrics are clinically distinct from PFAPA syndrome but retain an IL-1 signature

I Luu, J Nation, N Page, D Carvalho, A Magit… - Clinical …, 2021 - Elsevier
Autoinflammatory disorders of the innate immune system present with recurrent episodes of
inflammation often beginning in early childhood. While there are now more than 30 …

Children and adults with PFAPA syndrome: similarities and divergences in a real-life clinical setting

LL Sicignano, D Rigante, B Moccaldi, MG Massaro… - Advances in …, 2021 - Springer
Introduction Analogies or differences of periodic fever, aphthous stomatitis, pharyngitis, and
adenitis (PFAPA) syndrome in children and adults are barely known. The aim of our study …

[HTML][HTML] Does having MEFV gene sequence variants affect the clinical course and colchicine response in children with PFAPA syndrome?

G Otar Yener, İ Aktaş, C Altıntaş Meşe… - European Journal of …, 2023 - Springer
The primary aim of this study was to document the treatment modalities used in periodic
fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome and look for the …