Abstract von Hippel–Lindau (VHL) disease is an inheritable condition with an incidence of 1
in 36 000 live births. Individuals with VHL develop benign and malignant tumors including …

Von Hippel-Lindau disease (VHL) is one of the most common inherited neoplasia
syndromes and is characterized by highly vascular tumors of the eyes, brain, and spine, as …

Abstract von Hippel Lindau disease (vHL) is caused by a hereditary predisposition to
multiple neoplasms, especially hemangioblastomas in the retina and CNS, renal cell …

Object The tumors most frequently associated with von Hippel-Lindau (VHL) disease are
hemangioblastomas. While they are associated with significant neurological impairment and …

Background Historically, the survival of patients with von Hippel-Lindau disease (vHL) has
been poorer than that of the general population. We aimed to determine whether the survival …

Importance von Hippel–Lindau (VHL) disease–associated central nervous system (CNS)
lesions include hemangioblastomas and endolymphatic sac tumors (ELSTs), which are …

Von Hippel-Lindau (VHL) syndrome is characterized by hemangioblastomas of the brain,
spinal cord, and retina; renal cysts and clear cell renal cell carcinoma; pheochromocytoma …

Purpose To develop guidelines for ocular surveillance and early intervention for individuals
with von Hippel-Lindau (VHL) disease. Design Systematic review of the literature …

Objective: In a national retrospective cohort study, we aimed to determine the effect of
pregnancy on new von Hippel–Lindau (vHL) tumor development during pregnancy and at 1 …

Inspired by figure 3 in [13] Under normal circumstances, the wild type pVHL (VHL) interacts
with Elongin B (EB) and Elongin C (EC) to form the VBC-complex that in conjunction with …