Association of body mass index with clinical outcomes in patients with cystic fibrosis: a systematic review and meta-analysis

R Nagy, N Gede, K Ocskay, BM Dobai… - JAMA Network …, 2022 - jamanetwork.com
Importance The prevalence of overweight (body mass index [BMI]= 25-29.9 [calculated as
weight in kilograms divided by height in meters squared]) and obesity (BMI≥ 30) is …

ESPEN-ESPGHAN-ECFS guideline on nutrition care for cystic fibrosis

M Wilschanski, A Munck, E Carrion, M Cipolli, S Collins… - Clinical Nutrition, 2024 - Elsevier
Background Nutritional status is paramount in Cystic Fibrosis (CF) and is directly correlated
with morbidity and mortality. The first ESPEN-ESPGHAN-ECFS guidelines on nutrition care …

Gastrointestinal, pancreatic, and hepatic manifestations of cystic fibrosis in the newborn

G Galante, AJ Freeman - NeoReviews, 2019 - publications.aap.org
Gastrointestinal, pancreatic, and hepatic signs and symptoms represent the most common
presentation of early disease among patients with cystic fibrosis and may be the initial …

Effect of Trikafta on bone density, body composition and exercise capacity in CF: A pilot study

M Gur, R Bar–Yoseph, M Hanna… - Pediatric …, 2023 - Wiley Online Library
Background While the positive effect of Trikafta on cystic fibrosis (CF) pulmonary disease is
well established, there is limited data about its effect on bone mineral density (BMD), body …

The relationship between body composition, dietary intake, physical activity, and pulmonary status in adolescents and adults with cystic fibrosis

KJ Scully, LT Jay, S Freedman, GS Sawicki, A Uluer… - Nutrients, 2022 - mdpi.com
Measures of body fat and lean mass may better predict important clinical outcomes in
patients with cystic fibrosis (CF) than body mass index (BMI). Little is known about how diet …

[HTML][HTML] The association between body composition, leptin levels and glucose dysregulation in youth with cystic fibrosis

A Granados, EA Beach, AJ Christiansen… - Journal of Cystic …, 2021 - Elsevier
Background Optimization of nutritional status is recommended in patients with cystic fibrosis
(CF) given the association between lower body mass index (BMI) and poor clinical …

Usefulness of muscle ultrasonography in the nutritional assessment of adult patients with cystic fibrosis

FJ Sánchez-Torralvo, N Porras, I Ruiz-García… - Nutrients, 2022 - mdpi.com
Background: Muscle ultrasonography of the quadriceps rectus femoris (QRF) is a technique
on the rise in the assessment of muscle mass in application of nutritional assessment. The …

Gender Difference in the Relationship between Extrapulmonary Factors and Reduced Lung Function in Early Adulthood

K Doi, T Hirano, K Oishi, A Fukatsu-Chikumoto… - Journal of Clinical …, 2024 - mdpi.com
(1) Background: Reduced lung function in early adulthood is associated with future risks to
health outcomes that have not been fully explored by gender. We investigated gender …

Improvement in body composition following a supervised exercise-training program of adult patients with cystic fibrosis

A Prévotat, J Godin, H Bernard, T Perez… - … Medicine and Research, 2019 - Elsevier
Objectives Maintenance of optimal nutritional status is a crucial issue for cystic fibrosis (CF)
patients. Here, we evaluate the effects of an 8-week exercise training (ET) program on body …

Clinimetric evaluation of muscle function tests for individuals with cystic fibrosis: a systematic review

Y Combret, C Medrinal, T Bonnevie, FE Gravier… - Journal of Cystic …, 2020 - Elsevier
Accurate testing of muscle function is essential in individuals with cystic fibrosis (CF). A
literature search was conducted in MEDLINE, CENTRAL, CINAHL, PEDro, ScienceDirect …