Biomarkers and diagnostic guidelines for sporadic Creutzfeldt-Jakob disease

P Hermann, B Appleby, JP Brandel, B Caughey… - The Lancet …, 2021 - thelancet.com
Summary Sporadic Creutzfeldt-Jakob disease is a fatal neurodegenerative disease caused
by misfolded prion proteins (PrP Sc). Effective therapeutics are currently not available and …

Advanced tests for early and accurate diagnosis of Creutzfeldt–Jakob disease

G Zanusso, S Monaco, M Pocchiari… - Nature Reviews …, 2016 - nature.com
Early and accurate diagnosis of Creutzfeldt–Jakob disease (CJD) is a necessary to
distinguish this untreatable disease from treatable rapidly progressive dementias, and to …

Ultrasensitive RT-QuIC assay with high sensitivity and specificity for Lewy body-associated synucleinopathies

M Rossi, N Candelise, S Baiardi, S Capellari… - Acta …, 2020 - Springer
The clinical diagnosis of synucleinopathies, including Parkinson's disease (PD), dementia
with Lewy bodies (DLB), and multiple system atrophy (MSA), is challenging, especially at an …

Rapid and ultra-sensitive quantitation of disease-associated α-synuclein seeds in brain and cerebrospinal fluid by αSyn RT-QuIC

BR Groveman, CD Orrù, AG Hughson… - Acta neuropathologica …, 2018 - Springer
The diagnosis and treatment of synucleinopathies such as Parkinson disease and dementia
with Lewy bodies would be aided by the availability of assays for the pathogenic disease …

Diagnosis of human prion disease using real-time quaking-induced conversion testing of olfactory mucosa and cerebrospinal fluid samples

M Bongianni, C Orrù, BR Groveman… - JAMA …, 2017 - jamanetwork.com
Importance Early and accurate in vivo diagnosis of Creutzfeldt-Jakob disease (CJD) is
necessary for quickly distinguishing treatable from untreatable rapidly progressive …

Seed amplification and neurodegeneration marker trajectories in individuals at risk of prion disease

TH Mok, A Nihat, N Majbour, D Sequeira… - Brain, 2023 - academic.oup.com
Human prion diseases are remarkable for long incubation times followed typically by rapid
clinical decline. Seed amplification assays and neurodegeneration biofluid biomarkers are …

Seeding selectivity and ultrasensitive detection of tau aggregate conformers of Alzheimer disease

A Kraus, E Saijo, MA Metrick, K Newell… - Acta …, 2019 - Springer
Alzheimer disease (AD) and chronic traumatic encephalopathy (CTE) involve the abnormal
accumulation in the brain of filaments composed of both three-repeat (3R) and four-repeat …

Ultrasensitive and selective detection of 3-repeat tau seeding activity in Pick disease brain and cerebrospinal fluid

E Saijo, B Ghetti, G Zanusso, A Oblak, JL Furman… - Acta …, 2017 - Springer
The diagnosis and treatment of diseases involving tau-based pathology such as Alzheimer
disease and certain frontotemporal dementias is hampered by the inability to detect …

Prion seeding activity and infectivity in skin samples from patients with sporadic Creutzfeldt-Jakob disease

CD Orrú, J Yuan, BS Appleby, B Li, Y Li… - Science translational …, 2017 - science.org
Sporadic Creutzfeldt-Jakob disease (sCJD), the most common human prion disease, is
transmissible through iatrogenic routes due to abundant infectious prions [misfolded forms of …

A single ultrasensitive assay for detection and discrimination of tau aggregates of Alzheimer and Pick diseases

MA Metrick, NC Ferreira, E Saijo, A Kraus… - Acta neuropathologica …, 2020 - Springer
Multiple neurodegenerative diseases are characterized by aggregation of tau molecules.
Adult humans express six isoforms of tau that contain either 3 or 4 microtubule binding …