Sarcomas make up a broad group of malignant neoplasms of mesenchymal origin. More
than 70 histologic subtypes have been identified. However, sarcomas can be classified into …

Desmoid tumors (DT) are rare, locally aggressive, fibroblastic soft-tissue tumors that are
characterized by infiltrative growth and can affect organs and adjacent structures, resulting …

Hereditary colorectal cancer (HCRC) accounts for< 5% of all colorectal cancer cases. Some
of the unique characteristics commonly encountered in HCRC cases include early age of …

Desmoid tumors (DTs) are histologically benign proliferations of stromal cells but may grow
locally aggressive. Overall, DTs are rare (0.03% of all neoplasms). A minority of DTs is …

Familial adenomatous polyposis (FAP) and MUTYH-associated polyposis (MAP) are rare
inherited polyposis syndromes with a high colorectal cancer (CRC) risk. Therefore, frequent …

Purpose The optimal management of rare tumours (ie from accurate diagnosis to
management in reference centres) is a public health challenge. In 2009, the French National …

Familial adenomatous polyposis (FAP) is a well-described inherited syndrome,
characterized by the development of hundreds to thousands of adenomas in the colorectum …

It is estimated that 20% to 30% of colorectal cancers (CRCs) are familial with 5% to 10%
related to a known genetic syndrome. 1, 2 The hereditary CRCs are broadly divided into …

Familial adenomatous polyposis (FAP) is an autosomal dominant inherited syndrome
characterized by multiple adenomatous polyps (predisposing to colorectal cancer …

Desmoid tumors are rare soft tissue tumors that can have aggressive infiltrative growth and
relapse locally. Desmoid tumors can impact functionality and cause treatment-related …