Endometrial cancer in Lynch syndrome

S Zhao, L Chen, Y Zang, W Liu, S Liu… - … Journal of Cancer, 2022 - Wiley Online Library
Lynch syndrome (LS) is an autosomal dominant inherited disease caused by germline
pathogenic variants (PVs) in mismatch repair (MMR) genes. LS‐associated endometrial …

Genetic and genomic basis of the mismatch repair system involved in Lynch syndrome

K Tamura, M Kaneda, M Futagawa, M Takeshita… - International journal of …, 2019 - Springer
Lynch syndrome is a cancer-predisposing syndrome inherited in an autosomal-dominant
manner, wherein colon cancer and endometrial cancer develop frequently in the family, it …

[HTML][HTML] Splice modulators target PMS1 to reduce somatic expansion of the Huntington's disease-associated CAG repeat

ZL McLean, D Gao, K Correia, JCL Roy… - Nature …, 2024 - nature.com
Huntington's disease (HD) is a dominant neurological disorder caused by an expanded HTT
exon 1 CAG repeat that lengthens huntingtin's polyglutamine tract. Lowering mutant …

DNA mismatch repair and mutation avoidance pathways

TM Marti, C Kunz, O Fleck - Journal of cellular physiology, 2002 - Wiley Online Library
Unpaired and mispaired bases in DNA can arise by replication errors, spontaneous or
induced base modifications, and during recombination. The major pathway for correction of …

Structure of the MutL C‐terminal domain: a model of intact MutL and its roles in mismatch repair

A Guarné, S Ramon‐Maiques, EM Wolff… - The EMBO …, 2004 - embopress.org
MutL assists the mismatch recognition protein MutS to initiate and coordinate mismatch
repair in species ranging from bacteria to humans. The MutL N‐terminal ATPase domain is …

DNA mismatch repair defects: role in colorectal carcinogenesis

S Jacob, F Praz - Biochimie, 2002 - Elsevier
The inactivation of the DNA mismah repair (MMR) system, which is associated with the
predisposition to the hereditary non-polyposis colorectal cancer (HNPCC), has also been …

Functional significance and clinical phenotype of nontruncating mismatch repair variants of MLH1

TE Raevaara, MK Korhonen, H Lohi, H Hampel… - Gastroenterology, 2005 - Elsevier
Background & Aims: Germline mutations in mismatch repair genes are associated with
hereditary nonpolyposis colorectal cancer. A significant proportion of mutations are …

Mismatch Repair Gene PMS2 Disease-Causing Germline Mutations Are Frequent in Patients Whose Tumors Stain Negative for PMS2 Protein, but Paralogous Genes …

H Nakagawa, JC Lockman, WL Frankel, H Hampel… - Cancer Research, 2004 - AACR
The MutLα heterodimer formed by mismatch repair (MMR) proteins MLH1 and PMS2 is a
major component of the MMR complex, yet mutations in the PMS2 gene are rare in the …

A role for MLH3 in hereditary nonpolyposis colorectal cancer

Y Wu, MJW Berends, RH Sijmons, RGJ Mensink… - Nature …, 2001 - nature.com
We investigated a possible role of the mismatch-repair gene MLH3 in hereditary
nonpolyposis colorectal cancer by scanning for mutations in 39 HNPCC families and in 288 …

Expression of the MutL homologue hMLH3 in human cells and its role in DNA mismatch repair

E Cannavo, G Marra, J Sabates-Bellver, M Menigatti… - Cancer research, 2005 - AACR
The human mismatch repair (MMR) proteins hMLH1 and hPMS2 function in MMR as a
heterodimer. Cells lacking either protein have a strong mutator phenotype and display …