Cochlear implantation has become the standard‐of‐care for adults and children with severe
to profound hearing loss. There is growing evidence that qualitative as well as quantitative …

Auditory neuropathy spectrum disorder (ANSD) refers to a range of hearing impairments
characterized by deteriorated speech perception, despite relatively preserved pure-tone …

Hereditary Hearing Loss and Deafness Overview - Abstract - Europe PMC Sign in | Create an
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Congenital hearing loss affects one in 500 newborns. Sequence variations in OTOF, which
encodes the calcium-binding protein otoferlin, are responsible for 1–8% of congenital …

Pathological conditions in cochlea, such as ototoxicity, acoustic trauma, and age-related
cochlear degeneration, induce cell death in the organ of Corti and degeneration of the spiral …

The cochlear implant (CI) is widely considered to be one of the most innovative and
successful neuroprosthetic treatments developed to date. Although outcomes vary, CIs are …

Objective: To assess the efficacy of cochlear implantation (CI) after surgical removal of
sporadic intracochlear or intravestibulocochlear schwannomas. Study Design …

Importance In the US, most childhood-onset bilateral sensorineural hearing loss is genetic,
with more than 120 genes and thousands of different alleles known. Primary treatments are …

The indications for cochlear implantation have expanded over time due to evidence
demonstrating identification and implantation of appropriate cochlear implant (CI) …

Objectives: The variability in outcomes of cochlear implantation is largely unexplained, and
clinical factors are not sufficient for predicting performance. Genetic factors have been …