Recommendations for the management of hemophagocytic lymphohistiocytosis in adults

P La Rosée, AC Horne, M Hines… - Blood, The Journal …, 2019 - ashpublications.org
Hemophagocytic lymphohistiocytosis (HLH) is a severe hyperinflammatory syndrome
induced by aberrantly activated macrophages and cytotoxic T cells. The primary (genetic) …

Pediatric hemophagocytic lymphohistiocytosis

SW Canna, RA Marsh - Blood, The Journal of the American …, 2020 - ashpublications.org
Hemophagocytic lymphohistiocytosis (HLH) is a syndrome describing patients with severe
systemic hyperinflammation. Characteristic features include unremitting fever, cytopenias …

[HTML][HTML] Immune effector cell-associated hemophagocytic lymphohistiocytosis-like syndrome

MR Hines, TE Knight, KO McNerney, MB Leick… - … and Cellular Therapy, 2023 - Elsevier
Background T cell mediated hyperinflammatory responses such as cytokine release
syndrome (CRS) and immune effector cell associated neurotoxicity syndrome (ICANS) are …

Cytokine storm syndrome

RQ Cron, G Goyal, WW Chatham - Annual Review of Medicine, 2023 - annualreviews.org
Cytokine storm syndrome (CSS), which is frequently fatal, has garnered increased attention
with the ongoing coronavirus pandemic. A variety of hyperinflammatory conditions …

Histiocytic disorders

KL McClain, C Bigenwald, M Collin… - Nature Reviews …, 2021 - nature.com
The historic term 'histiocytosis' meaning 'tissue cell'is used as a unifying concept for
diseases characterized by pathogenic myeloid cells that share histological features with …

Ruxolitinib in adult patients with secondary haemophagocytic lymphohistiocytosis: an open-label, single-centre, pilot trial

A Ahmed, SA Merrill, F Alsawah… - The Lancet …, 2019 - thelancet.com
Background Hemophagocytic lymphohistiocytosis is a cytokine-driven inflammatory
syndrome that is associated with substantial morbidity and mortality. Overall survival in adult …

Interleukin-1 receptor blockade is associated with reduced mortality in sepsis patients with features of macrophage activation syndrome: reanalysis of a prior phase III …

B Shakoory, JA Carcillo, WW Chatham… - Critical care …, 2016 - journals.lww.com
Objective: To determine the efficacy of anakinra (recombinant interleukin-1 receptor
antagonist) in improving 28-day survival in sepsis patients with features of macrophage …

Weathering the COVID-19 storm: Lessons from hematologic cytokine syndromes

JT England, A Abdulla, CM Biggs, AYY Lee, KA Hay… - Blood Reviews, 2021 - Elsevier
A subset of patients with severe COVID-19 develop profound inflammation and multi-organ
dysfunction consistent with a “Cytokine Storm Syndrome”(CSS). In this review we compare …

Hemophagocytic lymphohistiocytosis

H Al-Samkari, N Berliner - Annual review of pathology …, 2018 - annualreviews.org
Hemophagocytic lymphohistiocytosis is a life-threatening disorder characterized by
unbridled activation of cytotoxic T lymphocytes, natural killer (NK) cells, and macrophages …

Hemophagocytic lymphohistiocytosis

TS Ponnatt, CM Lilley, KM Mirza - Archives of Pathology & …, 2022 - meridian.allenpress.com
Context.—Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening disorder of
immune regulation that can eventually result in end-organ damage and death. HLH is …