The epidemiology and clinical manifestations of autoimmunity in selective IgA deficiency
DD Odineal, ME Gershwin - Clinical Reviews in Allergy & Immunology, 2020 - Springer
Selective immunoglobulin A deficiency (SIgAD) is the most common primary
immunodeficiency, defined as an isolated deficiency of IgA (less than 0.07 g/L). Although the …
immunodeficiency, defined as an isolated deficiency of IgA (less than 0.07 g/L). Although the …
Lessons learned from the clinical presentation of common variable immunodeficiency disorders: a systematic review and meta-analysis
LMA Janssen, M van der Flier, E de Vries - Frontiers in immunology, 2021 - frontiersin.org
Background Diagnostic delay in common variable immunodeficiency disorders (CVID) is
considerable. There is no generally accepted symptom-recognition framework for its early …
considerable. There is no generally accepted symptom-recognition framework for its early …
[HTML][HTML] X-linked agammaglobulinemia (XLA): Phenotype, diagnosis, and therapeutic challenges around the world
ZA El-Sayed, I Abramova, JC Aldave, W Al-Herz… - World Allergy …, 2019 - Elsevier
Background X-linked agammaglobulinemia is an inherited immunodeficiency recognized
since 1952. In spite of seven decades of experience, there is still a limited understanding of …
since 1952. In spite of seven decades of experience, there is still a limited understanding of …
Autoimmunity in common variable immunodeficiency: epidemiology, pathophysiology and management
Introduction: Common variable immunodeficiency (CVID) comprises a large heterogeneous
group of patients with primary antibody deficiency. Areas covered: The affected patients are …
group of patients with primary antibody deficiency. Areas covered: The affected patients are …
[PDF][PDF] T-cell abnormalities in common variable immunodeficiency.
Common variable immunodeficiency (CVID) is the most common clinical primary
immunodeficiency. It is characterized by a defect in B-cell differentiation to plasma and …
immunodeficiency. It is characterized by a defect in B-cell differentiation to plasma and …
A high prevalence of gastrointestinal manifestations in common variable immunodeficiency
S Pikkarainen, T Martelius, A Ristimäki… - Official journal of the …, 2019 - journals.lww.com
OBJECTIVES: Common variable immunodeficiency (CVID) is associated with a spectrum of
autoimmune complications. We studied the prevalence of gastrointestinal (GI) …
autoimmune complications. We studied the prevalence of gastrointestinal (GI) …
Epidemiology and pathophysiology of malignancy in common variable immunodeficiency?
Common variable immunodeficiency (CVID) is a diagnostic category of primary
immunodeficiency (PID) which may present with heterogeneous disorders including …
immunodeficiency (PID) which may present with heterogeneous disorders including …
Approach to the management of autoimmunity in primary immunodeficiency
Primary immunodeficiency diseases (PID s) consist of a genetically heterogeneous group of
immune disorders that affect distinct elements of the immune system. PID patients are more …
immune disorders that affect distinct elements of the immune system. PID patients are more …
Evaluation of infectious and non-infectious complications in patients with primary immunodeficiency
Results: Infectious complications were more frequent than non-infectious complications.
Pneumonia and otitis media were the main infectious problems in PID patients, especially in …
Pneumonia and otitis media were the main infectious problems in PID patients, especially in …
Comparison of common monogenic defects in a large predominantly antibody deficiency cohort
Background Predominantly antibody deficiencies (PADs) are the most common primary
immunodeficiencies, characterized by hypogammaglobulinemia and inability to generate …
immunodeficiencies, characterized by hypogammaglobulinemia and inability to generate …